Mucocele of the appendix and pseudomyxoma peritonei are rare diseases. The clinical findings are nonspecific in the early stages of the disease. The sequelae of appendiceal mucocele, its perforation, and extensive peritoneal involvement via pseudomyxoma peritonei (jelly belly) are repeatedly described in the literature. We present the typical findings in the natural history of the disease.

1st Department of Surgery General University Hospital Prague 128 00 Prague Czech Republic

1st Faculty of Medicine Charles University 120 00 Prague Czech Republic

Departments of Radiodiagnostics General University Hospital Prague 128 00 Prague Czech Republic

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