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Low oxygen saturation following total correction in a patient with tetralogy of fallot and persistent left superior caval vein - how did we diagnose and manage?
Mehmet Turan Basunlu, Senay Coban, Gizem Sari, Turkay Saritas, Abdullah Erdem, Didem Melis Oztas, Metin Onur Beyaz, Emre Oteyaka, Yilmaz Yozgat, Murat Ugurlucan, Halil Turkoglu
Language English Country Czech Republic
Document type Case Reports
- Keywords
- nezastřešený koronární sinus,
- MeSH
- Heart Septal Defects, Atrial surgery pathology MeSH
- Tetralogy of Fallot * surgery pathology MeSH
- Infant MeSH
- Coronary Sinus MeSH
- Humans MeSH
- Treatment Outcome MeSH
- Check Tag
- Infant MeSH
- Humans MeSH
- Female MeSH
- Publication type
- Case Reports MeSH
Souvislost mezi Fallotovou tetralogií (tetralogy of Fallot, TOF) a jinými intrakardiálními patologiemi, jako jsou defekt septa síní (atrial septal defect, ASD), defekt síňokomorového kanálu nebo perzistentní levostranná horní dutá žíla (persistent left superior vena cava, PLSVC) i absence plicní chlopně, je dobře známa. Během chirurgického výkonu vyžadují přidružená onemocnění obzvláštní pozornost. V tomto článku popisujeme léčbu čtyřměsíční dívky s diagnózou TOF a PLSVC, u níž však byl přehlédnut nezastřešený koronární sinus. Nezastřešený koronární sinus se vyskytuje současně s TOF velmi vzácně.
Association of tetralogy of Fallot (TOF) with the other intracardiac pathologies such as atrial septal defect (ASD), atrioventricular canal defect or persistent left superior vena cava (PLSVC), absent pulmonary valve are well known pathologies. The associated pathologies require specific attention during surgical treatment. In this manuscript, we present management of a four-month-old girl who was diagnosed with TOF and PLSVC but the diagnosis of unroofed coronary sinus was missed in her. Association of unroofed coronary sinus with TOF is a very rare variant of TOF pathology.
Cardiovascular Surgery Clinic Istanbul Education and Research Hospital Istanbul Turkey
Department of Cardiovascular Surgery Faculty of Medicine Istanbul Medipol University Istanbul Turkey
Department of Cardiovascular Surgery Faculty of Medicine Mustafa Kemal University Hatay Turkey
Department of Pediatric Cardiology Faculty of Medicine Istanbul Medipol University Istanbul Turkey
References provided by Crossref.org
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