IgG4-related Diseases - A Rare Polycystic Form of Ormond's Disease
Language English Country Czech Republic Media print
Document type Case Reports, Journal Article
PubMed
27668529
DOI
10.14712/23362936.2016.13
PII: pmr_2016117020124
Knihovny.cz E-resources
- Keywords
- Ormond’s disease, Polycystic form, Retroperitoneal fibrosis,
- MeSH
- Immunoglobulin G * MeSH
- Middle Aged MeSH
- Humans MeSH
- Tomography, X-Ray Computed MeSH
- Retroperitoneal Fibrosis diagnosis pathology surgery MeSH
- Retroperitoneal Space pathology MeSH
- Urologic Surgical Procedures MeSH
- Check Tag
- Middle Aged MeSH
- Humans MeSH
- Male MeSH
- Publication type
- Journal Article MeSH
- Case Reports MeSH
- Names of Substances
- Immunoglobulin G * MeSH
Currently, Ormond's disease is classified among IgG4-associated diseases. Its clinical manifestation varies and is characterized by the presence of fibrous retroperitoneal tissue that often affects the ureters or abdominal aorta and iliac arteries. We present a unique case of the polycystic form of Ormond's disease, imitating tumour in the retroperitoneal space. At the time of diagnosis, the disease was not metabolically active and did not require immunosuppressive therapy. The polycystic mass was removed surgically. There has been no exacerbation of the disease during the last 12 months.
Department of Pathology Na Homolce Hospital Prague Czech Republic
Department of Vascular Surgery Na Homolce Hospital Prague Czech Republic
References provided by Crossref.org
