Unusual case of inflammatory rhabdomyoblastic tumor in a pediatric patient
Jazyk angličtina Země Německo Médium print-electronic
Typ dokumentu kazuistiky, časopisecké články
PubMed
37196469
DOI
10.1016/j.prp.2023.154524
PII: S0344-0338(23)00224-8
Knihovny.cz E-zdroje
- Klíčová slova
- Inflammatory leiomyosarcoma, Inflammatory rhabdomyoblastic tumor (IRMT), MLPA, Methylation SNP array, NGS,
- MeSH
- lidé MeSH
- nádorové biomarkery metabolismus MeSH
- nádory * MeSH
- Check Tag
- lidé MeSH
- Publikační typ
- časopisecké články MeSH
- kazuistiky MeSH
- Názvy látek
- nádorové biomarkery MeSH
Inflammatory rhabdomyoblastic tumor (IRMT) is a rare, recently described skeletal muscle neoplasm of uncertain malignant potential. We report an unusual tumor in the right arm of a 5-year-old boy, which is the first case of a pediatric IRMT. Immunohistochemically, most cells in the tumor were positive for CD163 and CD68 staining. The neoplastic cells themselves showed a skeletal muscle phenotype with a diffuse expression of desmin and a focal expression of myoD1. Mitotic activity was low (1/10 HPF), and no necrosis was observed.
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