Dystonin [dystonin]

topical
Terms

antigen BP 230
antigen bulózního pemfigoidu BPAG1

 

230 kDa Bullous Pemphigoid Antigen
230-240 kDa Bullous Pemphigoid Antigen
Bullous Pemphigoid Antigen 1
Hemidesmosomal Plaque Protein

Definition

A plakin characterized by repeat sequences homologous to SPECTRIN and PLECTIN and C-terminal EF HAND MOTIFS. It functions as an integrator of INTERMEDIATE FILAMENTS, ACTIN and MICROTUBULES in cytoskeleton networks. It is required for anchoring intermediate filaments to the actin cytoskeleton in neural and muscle cells as well as anchoring KERATIN-containing intermediate filaments to HEMIDESMOSOMES in EPITHELIAL CELLS.

DUI
D000071821 MeSH Browser
CUI
M000615558
Previous indexing
Carrier Proteins (1995-2016); Cytoskeletal Proteins (1995-2016); Nerve Tissue Proteins (1995-2016)
History note
2017
Public note
2017

DST protein, human Chemical MeSH Browser

Dst protein, mouse Chemical MeSH Browser

Dst protein, rat Chemical MeSH Browser