Hypoadrenocorticism, Familial [familiární hypoadrenokorticismus]

topical
Terms

Addison Disease, X-Linked
Adrenal Hypoplasia, Congenital
Adrenal Hypoplasia, Congenital, with Hypogonadotropic Hypogonadism
AHC with Isolated Gonadotropin Deficiency
Complex Glycerol Kinase Deficiency
Cytomegalic Adrenocortical Hypoplasia
Familial X-linked Addison Disease
X-linked Adrenal Hypoplasia
X-linked Congenital Adrenal Hypoplasia
Xp21 Contiguous Gene Deletion Syndrome

Definition

Genetic or familial occurrence of ADDISONS DISEASE characterized by insufficient production of cortisol, aldosterone, and/or other hormones made in the adrenal cortex.

DUI
D000075262 MeSH Browser
CUI
M000630038
History note
2018(2010)
Public note
2018; HYPOADRENOCORTICISM, FAMILIAL was indexed under ADRENAL INSUFFICIENCY 2010-2017