fibrózní dysplazie polyostotická [Fibrous Dysplasia, Polyostotic]
- Termíny
-
McCune-Albrightův syndrom
McCuneův-Albrightův syndrom
polyostotická fibrózní dysplazie kostí
-
Albright Syndrome
Albright-Mccune-Sternberg Syndrome
Albright-Sternberg Syndrome
Albright's Disease
Albright's Disease of Bone
Albright's Syndrome
Albright's Syndrome with Precocious Puberty
Fibrous Dysplasia with Pigmentary Skin Changes and Precocious Puberty
McCune-Albright Syndrome
Polyostotic Fibrous Dysplasia
Kostní tkáň je částečně nahrazována vazivem. Nemoc začíná mezi 5. a 15. rokem, projevuje se bolestmi kostí a spontánními frakturami. (cit. Velký lékařský slovník online, 2016 http://lekarske.slovniky.cz)
FIBROUS DYSPLASIA OF BONE affecting several bones. When melanotic pigmentation (CAFE-AU-LAIT SPOTS) and multiple endocrine hyperfunction are additionally associated it is referred to as Albright syndrome.
- Anotace
- sometimes Jaffe-Lichtenstein (usually monostotic) goes here: check text; craniofacial fibrous dysplasia: coord IM with FACIAL BONES (IM) + SKULL (IM)
- DUI
- D005359 MeSH Prohlížeč
- CUI
- M0008457
- Historická pozn.
- 91(75); was see under FIBROUS DYSPLASIA OF BONE 1967-90; ALBRIGHT'S DISEASE & JAFFE-LICHTENSTEIN DISEASE were see under OSTEITIS FIBROSA 1963-66
- Online pozn.
- use FIBROUS DYSPLASIA OF BONE to search FIBROUS DYSPLASIA, POLYOSTOTIC 1967-74; search ALBRIGHT'S DISEASE & JAFFE-LICHTENSTEIN DISEASE under OSTEITIS FIBROSA CYSTICA 1966
- Veřejná pozn.
- 91; was see under FIBROUS DYSPLASIA OF BONE 1967-90; ALBRIGHT'S DISEASE & JAFFE-LICHTENSTEIN DISEASE were see under OSTEITIS FIBROSA 1963-66
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