G(M3) Ganglioside [G(M3) gangliosid]

topical
2
Terms

Ganglioside GM3
Hematoside
II3NeuAcLacCer
Sialyl Lactosylceramide
Sialyllactosylceramide

Persistent link   https://www.medvik.cz/link/D005679
Definition

A ganglioside present in abnormally large amounts in the brain and liver due to a deficient biosynthetic enzyme, G(M3):UDP-N-acetylgalactosaminyltransferase. Deficiency of this enzyme prevents the formation of G(M2) ganglioside from G(M3) ganglioside and is the cause of an anabolic sphingolipidosis.

Annotation
G(M3) gangliosidosis: coord NIM with GANGLIOSIDOSIS (IM)
DUI
D005679 MeSH Browser
CUI
M0008926
Previous indexing
Gangliosides (1966-1976)
History note
91(77); was see under GANGLIOSIDES 1977-90
Public note
91; was see under GANGLIOSIDES 1977-90

D Chemicals and Drugs
D09.400.410 Glycolipids 74
D09.400.410.420 Glycosphingolipids 46
D09.400.410.420.025 Acidic Glycosphingolipids 1
D09.400.410.420.025.475 Gangliosides 42
D09.400.410.420.025.475.390 G(M1) Ganglioside 17
D09.400.410.420.025.475.400 G(M2) Ganglioside 7
D09.400.410.420.025.475.510 G(M3) Ganglioside 2
D10 Lipids 2 524
D10.390 Glycolipids 74
D10.390.470 Glycosphingolipids 46
D10.390.470.025 Acidic Glycosphingolipids 1
D10.390.470.025.475 Gangliosides 42
D10.390.470.025.475.390 G(M1) Ganglioside 17
D10.390.470.025.475.400 G(M2) Ganglioside 7
D10.390.470.025.475.510 G(M3) Ganglioside 2
D10.570 Membrane Lipids 260
D10.570.877 Sphingolipids 65
D10.570.877.360 Glycosphingolipids 46
D10.570.877.360.025 Acidic Glycosphingolipids 1
D10.570.877.360.025.475 Gangliosides 42
D10.570.877.360.025.475.390 G(M1) Ganglioside 17
D10.570.877.360.025.475.400 G(M2) Ganglioside 7
D10.570.877.360.025.475.510 G(M3) Ganglioside 2