Trihexosylceramides [trihexosylceramidy]

topical
11
Terms

Ceramide Trihexosides
Trihexosyl Ceramides

Persistent link   https://www.medvik.cz/link/D014281
Definition

Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE).

Annotation
/biosyn /physiol permitted
DUI
D014281 MeSH Browser
CUI
M0021970
Previous indexing
Ceramides (1972-1978); Cerebrosides (1966-1978); Glycosphingolipids (1975-1978)
History note
91(79); was see under GLYCOSPHINGOLIPIDS 1979-90
Public note
91; was see under GLYCOSPHINGOLIPIDS 1979-90

D Chemicals and Drugs
D02.065 Amides 260
D02.065.313 Ceramides 92
D02.065.313.250 Cerebrosides 5
D02.065.313.425 Globosides 1
D02.065.313.612 Lactosylceramides 3
D02.065.313.906 Trihexosylceramides 11
D09.400.410 Glycolipids 74
D09.400.410.420 Glycosphingolipids 46
D09.400.410.420.525 Neutral Glycosphingolipids 2
D09.400.410.420.525.200 Ceramides 92
D09.400.410.420.525.200.250 Cerebrosides 5
D09.400.410.420.525.200.425 Globosides 1
D09.400.410.420.525.200.612 Lactosylceramides 3
D09.400.410.420.525.200.906 Trihexosylceramides 11
D10 Lipids 2 528
D10.390 Glycolipids 74
D10.390.470 Glycosphingolipids 46
D10.390.470.675.200 Ceramides 92
D10.390.470.675.200.250 Cerebrosides 5
D10.390.470.675.200.425 Globosides 1
D10.390.470.675.200.612 Lactosylceramides 3
D10.390.470.675.200.906 Trihexosylceramides 11
D10.570 Membrane Lipids 261
D10.570.877 Sphingolipids 65
D10.570.877.360 Glycosphingolipids 46
D10.570.877.360.612 Neutral Glycosphingolipids 2
D10.570.877.360.612.200 Ceramides 92
D10.570.877.360.612.200.250 Cerebrosides 5
D10.570.877.360.612.200.425 Globosides 1
D10.570.877.360.612.200.612 Lactosylceramides 3
D10.570.877.360.612.200.906 Trihexosylceramides 11

adamantyl-globotriaosyl ceramide Chemical MeSH Browser

corrugoside Chemical MeSH Browser

globotriaosylceramide Chemical MeSH Browser

globotrihexosylceramide Chemical MeSH Browser

isoglobotrihexosylceramide Chemical MeSH Browser

lissamine rhodamine sulfonylamidosphingosyl-trihexosylceramide Chemical MeSH Browser

neogalatriaosylceramide Chemical MeSH Browser

thioisoglobotrihexosylceramide Chemical MeSH Browser