Phosphofructokinase-1, Muscle Type [svalová fosfofruktokinasa-1]

topical
Terms

6-fosfofruktokinasa - svalový typ
fosfofruktokinasa-1 - svalový typ
svalová fosfofruktokináza 1
svalová fosfofruktokináza-1

 

6-Phosphofructokinase, Muscle Type
Phosphofructo-1-kinase Isozyme A

Persistent link   https://www.medvik.cz/link/D025203
Definition

An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. In humans, PHOSPHOFRUCTOKINASE-1 in muscle exists as the homotetramer of M subunits. Defects in this muscle enzyme cause GLYCOGEN STORAGE DISEASE TYPE VII, also known as Tarui's disease.

DUI
D025203 MeSH Browser
CUI
M0373928
Previous indexing
6-Phosphofructokinase (1977-2001)
History note
2002
Public note
2002

PFKM protein, human Chemical MeSH Browser

phosphofructokinase-1 subunit, type M Chemical MeSH Browser