Methylmalonate-Semialdehyde Dehydrogenase (Acylating) [methylmalonát-semialdehyddehydrogenasa (acylační)]

topical
Terms

metylmalonát-semialdehyddehydrogenáza (acylační)
MMSDH

 

Methylmalonic-Semialdehyde Dehydrogenase (Acylating)
MMSA Dehydrogenase
MMSDH

Persistent link   https://www.medvik.cz/link/D050646
Definition

An enzyme that plays a role in the VALINE; LEUCINE; and ISOLEUCINE catabolic pathways by catalyzing the oxidation of 2-methyl-3-oxopropanate to propanoyl-CoA using NAD+ as a coenzyme. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated BETA-ALANINE and 3-hydropropionic acid.

DUI
D050646 MeSH Browser
CUI
M0144948
History note
2006(1987)
Public note
2006; METHYLMALONATE-SEMIALDEHYDE DEHYDROGENASE (ACYLATING) was indexed under ALDEHYDE OXIDOREDUCTASES 1987-2005

D Chemicals and Drugs
D08.811 Enzymes 1 551
D08.811.682 Oxidoreductases 446
D08.811.682.657.163 Aldehyde Oxidoreductases 25
D08.811.682.657.163.249 Aldehyde Dehydrogenase 38
D08.811.682.657.163.311 Aldehyde Oxidase 4
D08.811.682.657.163.374 Aspartate-Semialdehyde Dehydrogenase 1
D08.811.682.657.163.468 Benzaldehyde Dehydrogenase (NADP+)
D08.811.682.657.163.515 Betaine-Aldehyde Dehydrogenase
D08.811.682.657.163.781 Glycolaldehyde Dehydrogenase 1
D08.811.682.657.163.843 Succinate-Semialdehyde Dehydrogenase 1
D10 Lipids 2 528