Acid Ceramidase [kyselá ceramidasa]

topical
6
Terms

kyselá ceramidáza

Persistent link   https://www.medvik.cz/link/D055573
Definition

A ceramidase subtype that is active at acid pH. It plays an important role in sphingolipid degradation by catalyzing the lysosomal hydrolysis of ceramide to sphingosine and free fatty acid. Inherited deficiency of acid ceramidase activity results in FARBER LIPOGRANULOMATOSIS.

DUI
D055573 MeSH Browser
CUI
M0518530
Previous indexing
Galactosylgalactosylglucosylceramidase (1974-2008)
History note
2009(1982); use GALACTOSYLGALACTOSYLGLUCOSYLCERAMIDASE 1983-2008
Public note
2009; see CERAMIDE TRIHEXOSIDASE 1983-2008

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Asah1 protein, rat Chemical MeSH Browser