Hamman-Rich Syndrome [Hammanův-Richův syndrom]

topical
1
Terms

akutní intersticiální pneumonie
akutní intersticiální pneumonitida
Hammanova-Richova nemoc

 

Acute Interstitial Pneumonia
Acute Interstitial Pneumonitis
Hamman-Rich Disease

Definition

Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

DUI
D000080203 MeSH Browser
CUI
M000646521
History note
2020; for HAMMAN-RICH SYNDROME use PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME use IDIOPATHIC PULMONARY FIBROSIS 2010-2019
Public note
for HAMMAN-RICH SYNDROME see PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME see IDIOPATHIC PULMONARY FIBROSIS 2010-2019