Hearing Loss, Sensorineural [percepční nedoslýchavost]

topical
92
Terms

kochleární nedoslýchavost
kochleární porucha sluchu
kochleární ztráta sluchu
nedoslýchavost percepční
nedoslýchavost senzorineurální
senzorineurální nedoslýchavost
senzorineurální porucha sluchu
senzorineurální ztráta sluchu

 

Cochlear Hearing Loss
Deafness Neurosensory
Deafness, Neurosensory
Deafness, Sensoryneural
Hearing Loss, Cochlear
Neurosensory Deafness
Sensorineural Hearing Loss
Sensoryneural Deafness

Persistent link   https://www.medvik.cz/link/D006319
Definition

Hearing loss resulting from damage to the COCHLEA and the sensorineural elements which lie internally beyond the oval and round windows. These elements include the AUDITORY NERVE and its connections in the BRAINSTEM.

Annotation
HEARING LOSS, MIXED CONDUCTIVE-SENSORINEURAL is also available
DUI
D006319 MeSH Browser
CUI
M0009934
Previous indexing
Deafness (1966-1978)
History note
79
Public note
79

C Diseases
C09.218 Ear Diseases 316
C09.218.458 Hearing Disorders 1 299
C09.218.458.341 Hearing Loss 217
C09.218.458.341.186 Deafness 435
C09.218.458.341.374 Hearing Loss, Bilateral 12
C09.218.458.341.562 Hearing Loss, Conductive 32
C09.218.458.341.750 Hearing Loss, Functional 2
C09.218.458.341.812 Hearing Loss, High-Frequency 3
C09.218.458.341.887 Hearing Loss, Sensorineural 92
C09.218.458.341.887.432 Hearing Loss, Central 2
C09.218.458.341.887.460 Hearing Loss, Noise-Induced 107
C09.218.458.341.887.772 Presbycusis 33
C09.218.458.341.887.886 Usher Syndromes 8
C09.218.458.341.900 Hearing Loss, Sudden 32
C09.218.458.341.950 Hearing Loss, Unilateral 17
C09.218.458.341.975 Hearing Loss, Hidden
C10.597.751 Sensation Disorders 94
C10.597.751.418 Hearing Disorders 1 299
C10.597.751.418.341 Hearing Loss 217
C10.597.751.418.341.186 Deafness 435
C10.597.751.418.341.374 Hearing Loss, Bilateral 12
C10.597.751.418.341.562 Hearing Loss, Conductive 32
C10.597.751.418.341.750 Hearing Loss, Functional 2
C10.597.751.418.341.812 Hearing Loss, High-Frequency 3
C10.597.751.418.341.887 Hearing Loss, Sensorineural 92
C10.597.751.418.341.887.432 Hearing Loss, Central 2
C10.597.751.418.341.887.460 Hearing Loss, Noise-Induced 107
C10.597.751.418.341.887.772 Presbycusis 33
C10.597.751.418.341.887.886 Usher Syndromes 8
C10.597.751.418.341.900 Hearing Loss, Sudden 32
C10.597.751.418.341.950 Hearing Loss, Unilateral 17
C10.597.751.418.341.975 Hearing Loss, Hidden
C23.888 Signs and Symptoms 3 919
C23.888.592 Neurologic Manifestations 1 055
C23.888.592.763 Sensation Disorders 94
C23.888.592.763.393 Hearing Disorders 1 299
C23.888.592.763.393.341 Hearing Loss 217
C23.888.592.763.393.341.186 Deafness 435
C23.888.592.763.393.341.374 Hearing Loss, Bilateral 12
C23.888.592.763.393.341.562 Hearing Loss, Conductive 32
C23.888.592.763.393.341.750 Hearing Loss, Functional 2
C23.888.592.763.393.341.812 Hearing Loss, High-Frequency 3
C23.888.592.763.393.341.887 Hearing Loss, Sensorineural 92
C23.888.592.763.393.341.887.432 Hearing Loss, Central 2
C23.888.592.763.393.341.887.460 Hearing Loss, Noise-Induced 107
C23.888.592.763.393.341.887.772 Presbycusis 33
C23.888.592.763.393.341.887.886 Usher Syndromes 8
C23.888.592.763.393.341.900 Hearing Loss, Sudden 32
C23.888.592.763.393.341.950 Hearing Loss, Unilateral 17
C23.888.592.763.393.341.975 Hearing Loss, Hidden

Acrootoocular Syndrome Disease MeSH Browser

Albinism ocular late onset sensorineural deafness Disease MeSH Browser

Arthrogryposis-like hand anomaly and sensorineural deafness Disease MeSH Browser

Ataxia, Deafness, and Cardiomyopathy Disease MeSH Browser

Athabaskan brainstem dysgenesis Disease MeSH Browser

Atherosclerosis, Premature, with Deafness, Nephropathy, Diabetes Mellitus, Photomyoclonus, and Degenerative Neurologic Disease Disease MeSH Browser

Auditory Neuropathy, Nonsyndromic Recessive Disease MeSH Browser

Axenfeld-Rieger Anomaly with Partially Absent Eye Muscles, Distinctive Face, Hydrocephaly, and Skeletal Abnormalities Disease MeSH Browser

Axenfeld-Rieger anomaly with cardiac defects and sensorineural hearing loss Disease MeSH Browser

BADS Syndrome Disease MeSH Browser

Barakat syndrome Disease MeSH Browser

Bartter Syndrome, Type 4A Disease MeSH Browser

Bartter Syndrome, Type 4b Disease MeSH Browser

Bjornstad syndrome Disease MeSH Browser

Boudhina Yedes Khiari syndrome Disease MeSH Browser

Brachydactyly, Intraventricular Septal Defect, And Deafness Disease MeSH Browser

Brown-Vialetto-Van Laere syndrome Disease MeSH Browser

CAPOS syndrome Disease MeSH Browser

Cardiomyopathy, Dilated, 1J Disease MeSH Browser

Cataract ataxia deafness Disease MeSH Browser

Cataracts, Congenital, with Sensorineural Deafness, Down Syndrome-Like Facial Appearance, Short Stature, and Mental Retardation Disease MeSH Browser

Cerebellar Ataxia and Hypergonadotropic Hypogonadism Disease MeSH Browser

Cerebellar Ataxia and Neurosensory Deafness Disease MeSH Browser

Cerebellar Ataxia, Deafness, and Narcolepsy Disease MeSH Browser

Charcot-Marie-Tooth disease and deafness Disease MeSH Browser

Charcot-Marie-Tooth disease, Type 2J Disease MeSH Browser

Chitty Hall Baraitser syndrome Disease MeSH Browser

Chudley-Mccullough syndrome Disease MeSH Browser

Cleft palate, midfacial hypoplasia, triangular facies, and sensorineural hearing loss Disease MeSH Browser

Cochleosaccular degeneration of the inner ear and progressive cataracts Disease MeSH Browser

Coloboma, cleft lip-palate and mental retardation syndrome Disease MeSH Browser

Congenital ectodermal dysplasia with hearing loss Disease MeSH Browser

Corneal dystrophy and perceptive deafness Disease MeSH Browser

Cowchock syndrome Disease MeSH Browser

Craniofacial deafness hand syndrome Disease MeSH Browser

Cutis Verticis Gyrata, Retinitis Pigmentosa, and Sensorineural Deafness Disease MeSH Browser

Deafness enamel hypoplasia nail defects Disease MeSH Browser

Deafness oligodontia syndrome Disease MeSH Browser

Deafness, Autosomal Dominant 1 Disease MeSH Browser

Deafness, Autosomal Dominant 10 Disease MeSH Browser

Deafness, Autosomal Dominant 11 Disease MeSH Browser

Deafness, Autosomal Dominant 12 Disease MeSH Browser

Deafness, Autosomal Dominant 13 Disease MeSH Browser

Deafness, Autosomal Dominant 15 Disease MeSH Browser

Deafness, Autosomal Dominant 16 Disease MeSH Browser

Deafness, Autosomal Dominant 18 Disease MeSH Browser

Deafness, Autosomal Dominant 20 Disease MeSH Browser

Deafness, Autosomal Dominant 21 Disease MeSH Browser

Deafness, Autosomal Dominant 23 Disease MeSH Browser

Deafness, Autosomal Dominant 24 Disease MeSH Browser

Deafness, Autosomal Dominant 25 Disease MeSH Browser

Deafness, Autosomal Dominant 28 Disease MeSH Browser

Deafness, Autosomal Dominant 2A Disease MeSH Browser

Deafness, Autosomal Dominant 2B Disease MeSH Browser

Deafness, Autosomal Dominant 30 Disease MeSH Browser

Deafness, Autosomal Dominant 31 Disease MeSH Browser

Deafness, Autosomal Dominant 36 Disease MeSH Browser

Deafness, Autosomal Dominant 39, with Dentinogenesis Imperfecta 1 Disease MeSH Browser

Deafness, Autosomal Dominant 3A Disease MeSH Browser

Deafness, Autosomal Dominant 3B Disease MeSH Browser

Deafness, Autosomal Dominant 4 Disease MeSH Browser

Deafness, Autosomal Dominant 41 Disease MeSH Browser

Deafness, Autosomal Dominant 43 Disease MeSH Browser

Deafness, Autosomal Dominant 44 Disease MeSH Browser

Deafness, Autosomal Dominant 47 Disease MeSH Browser

Deafness, Autosomal Dominant 48 Disease MeSH Browser

Deafness, Autosomal Dominant 49 Disease MeSH Browser

Deafness, Autosomal Dominant 5 Disease MeSH Browser

Deafness, Autosomal Dominant 52 Disease MeSH Browser

Deafness, Autosomal Dominant 53 Disease MeSH Browser

Deafness, Autosomal Dominant 59 Disease MeSH Browser

Deafness, Autosomal Dominant 6 Disease MeSH Browser

Deafness, Autosomal Dominant 7 Disease MeSH Browser

Deafness, Autosomal Dominant 9 Disease MeSH Browser

Deafness, Autosomal Recessive Disease MeSH Browser

Deafness, Autosomal Recessive 10 Disease MeSH Browser

Deafness, Autosomal Recessive 12 Disease MeSH Browser

Deafness, Autosomal Recessive 13 Disease MeSH Browser

Deafness, Autosomal Recessive 14 Disease MeSH Browser

Deafness, Autosomal Recessive 15 Disease MeSH Browser

Deafness, Autosomal Recessive 16 Disease MeSH Browser

Deafness, Autosomal Recessive 17 Disease MeSH Browser

Deafness, Autosomal Recessive 18 Disease MeSH Browser

Deafness, Autosomal Recessive 1A Disease MeSH Browser

Deafness, Autosomal Recessive 1b Disease MeSH Browser

Deafness, Autosomal Recessive 2 Disease MeSH Browser

Deafness, Autosomal Recessive 20 Disease MeSH Browser

Deafness, Autosomal Recessive 21 Disease MeSH Browser

Deafness, Autosomal Recessive 22 Disease MeSH Browser

Deafness, Autosomal Recessive 23 Disease MeSH Browser

Deafness, Autosomal Recessive 26 Disease MeSH Browser

Deafness, Autosomal Recessive 27 Disease MeSH Browser

Deafness, Autosomal Recessive 28 Disease MeSH Browser

Deafness, Autosomal Recessive 3 Disease MeSH Browser

Deafness, Autosomal Recessive 30 Disease MeSH Browser

Deafness, Autosomal Recessive 31 Disease MeSH Browser

Deafness, Autosomal Recessive 32 Disease MeSH Browser

Deafness, Autosomal Recessive 33 Disease MeSH Browser

Deafness, Autosomal Recessive 35 Disease MeSH Browser

Deafness, Autosomal Recessive 36 Disease MeSH Browser

Deafness, Autosomal Recessive 37 Disease MeSH Browser

Deafness, Autosomal Recessive 38 Disease MeSH Browser

Deafness, Autosomal Recessive 39 Disease MeSH Browser

Deafness, Autosomal Recessive 4 Disease MeSH Browser

Deafness, Autosomal Recessive 40 Disease MeSH Browser

Deafness, Autosomal Recessive 42 Disease MeSH Browser

Deafness, Autosomal Recessive 44 Disease MeSH Browser

Deafness, Autosomal Recessive 46 Disease MeSH Browser

Deafness, Autosomal Recessive 47 Disease MeSH Browser

Deafness, Autosomal Recessive 48 Disease MeSH Browser

Deafness, Autosomal Recessive 49 Disease MeSH Browser

Deafness, Autosomal Recessive 5 Disease MeSH Browser

Deafness, Autosomal Recessive 53 Disease MeSH Browser

Deafness, Autosomal Recessive 59 Disease MeSH Browser

Deafness, Autosomal Recessive 6 Disease MeSH Browser

Deafness, Autosomal Recessive 62 Disease MeSH Browser

Deafness, Autosomal Recessive 63 Disease MeSH Browser

Deafness, Autosomal Recessive 65 Disease MeSH Browser

Deafness, Autosomal Recessive 66 Disease MeSH Browser

Deafness, Autosomal Recessive 67 Disease MeSH Browser

Deafness, Autosomal Recessive 68 Disease MeSH Browser

Deafness, Autosomal Recessive 7 Disease MeSH Browser

Deafness, Autosomal Recessive 71 Disease MeSH Browser

Deafness, Autosomal Recessive 77 Disease MeSH Browser

Deafness, Autosomal Recessive 79 Disease MeSH Browser

Deafness, Autosomal Recessive 9 Disease MeSH Browser

Deafness, Autosomal Recessive, 24 Disease MeSH Browser

Deafness, Childhood-Onset Neurosensory, Autosomal Recessive 8 Disease MeSH Browser

Deafness, Congenital, with Inner Ear Agenesis, Microtia, and Microdontia Disease MeSH Browser

Deafness, High-Frequency Sensorineural, X-Linked Disease MeSH Browser

Deafness, Progressive High-Tone Neural Disease MeSH Browser

Deafness, Sensorineural, And Male Infertility Disease MeSH Browser

Deafness, Sensorineural, Autosomal-Mitochondrial Type Disease MeSH Browser

Deafness, Sensorineural, with Hypertrophic Cardiomyopathy Disease MeSH Browser

Deafness, Sensorineural, with Peripheral Neuropathy and Arterial Disease Disease MeSH Browser

Deafness, X-Linked 1 Disease MeSH Browser

Deafness, X-Linked 3 Disease MeSH Browser

Deafness, X-Linked 4 Disease MeSH Browser

Deafness, X-Linked 5 Disease MeSH Browser

Deafness, autosomal dominant nonsyndromic sensorineural 17 Disease MeSH Browser

Deafness, autosomal dominant nonsyndromic sensorineural 22 Disease MeSH Browser

Deafness, autosomal dominant nonsyndromic sensorineural 23 Disease MeSH Browser

Deafness, autosomal dominant nonsyndromic sensorineural 24 Disease MeSH Browser

Digitorenocerebral Syndrome Disease MeSH Browser

Donnai-Barrow syndrome Disease MeSH Browser

Ectodermal Dysplasia and Neurosensory Deafness Disease MeSH Browser

Ectodermal dysplasia, sensorineural hearing loss, and distinctive facial features Disease MeSH Browser

Ermine phenotype Disease MeSH Browser

Fitzsimmons Walson Mellor syndrome Disease MeSH Browser

Flynn Aird syndrome Disease MeSH Browser

Friedreich Ataxia, So-Called, with Optic Atrophy and Sensorineural Deafness Disease MeSH Browser

Gemignani syndrome Disease MeSH Browser

Gonadal dysgenesis XX type deafness Disease MeSH Browser

Griscelli syndrome type 1 Disease MeSH Browser

HID Syndrome Disease MeSH Browser

Histiocytosis with joint contractures and sensorineural deafness Disease MeSH Browser

Hittner Hirsch Kreh syndrome Disease MeSH Browser

Homozygous 11p15-p14 Deletion Syndrome Disease MeSH Browser

Insulin-Like Growth Factor I Deficiency Disease MeSH Browser

Johanson Blizzard syndrome Disease MeSH Browser

Knuckle pads, leuconychia and sensorineural deafness Disease MeSH Browser

Lipodystrophy, Generalized, with Mental Retardation, Deafness, Short Stature, and Slender Bones Disease MeSH Browser

MYH9-Related Disorders Disease MeSH Browser

Macrothrombocytopenia progressive deafness Disease MeSH Browser

Marshall syndrome Disease MeSH Browser

Martin-Probst Deafness-Mental Retardation Syndrome Disease MeSH Browser

Nephropathy deafness hyperparathyroidism Disease MeSH Browser

Nephropathy with Pretibial Epidermolysis Bullosa and Deafness Disease MeSH Browser

Nephropathy, Progressive, with Deafness Disease MeSH Browser

Neuroendocrine Carcinoma of Salivary Glands, Sensorineural Hearing Loss, and Enamel Hypoplasia Disease MeSH Browser

Nonsyndromic sensorineural hearing loss Disease MeSH Browser

Optic Atrophy, Deafness, Ophthalmoplegia, and Myopathy Disease MeSH Browser

Optic atrophy 1 and deafness Disease MeSH Browser

Otodental Dysplasia Disease MeSH Browser

Otofacioosseous-Gonadal Syndrome Disease MeSH Browser

Palmoplantar Keratoderma with Deafness Disease MeSH Browser

Paragangliomas with Sensorineural Hearing Loss Disease MeSH Browser

Pendred syndrome Disease MeSH Browser

Pfeiffer Kapferer syndrome Disease MeSH Browser

Progressive hearing loss stapes fixation Disease MeSH Browser

Prune Belly Syndrome with Pulmonic Stenosis, Mental Retardation, and Deafness Disease MeSH Browser

Renal Tubular Acidosis, Distal, Autosomal Recessive, with Late-Onset Sensorineural Hearing Loss Disease MeSH Browser

Renal Tubular Acidosis, Distal, with Progressive Nerve Deafness Disease MeSH Browser

Retinitis Pigmentosa Inversa with Deafness Disease MeSH Browser

Robinson Miller Bensimon syndrome Disease MeSH Browser

Rod-Cone Dystrophy, Sensorineural Deafness, and Fanconi-Type Renal Dysfunction Disease MeSH Browser

Schaap Taylor Baraitser syndrome Disease MeSH Browser

SeSAME syndrome Disease MeSH Browser

Sensorineural Deafness With Mild Renal Dysfunction Disease MeSH Browser

Sensorineural Hearing Loss, Retinal Pigment Epithelium Lesions, Discolored Teeth Disease MeSH Browser

Spastic Paraplegia, Sensorineural Deafness, Mental Retardation, And Progressive Nephropathy Disease MeSH Browser

Split-Hand-Foot Malformation With Sensorineural Hearing Loss Disease MeSH Browser

Spondyloepiphyseal Dysplasia, Myopia, And Sensorineural Deafness Disease MeSH Browser

Stickler Syndrome, Autosomal Recessive, COL9A1-Related Disease MeSH Browser

Stickler syndrome, type 1 Disease MeSH Browser

Thiamine responsive megaloblastic anemia syndrome Disease MeSH Browser

Townes-Brocks syndrome Disease MeSH Browser

Townes-Brocks-Branchiootorenal-Like Syndrome Disease MeSH Browser

Treft Sanborn Carey syndrome Disease MeSH Browser

Tunglang Savage Bellman syndrome Disease MeSH Browser

Vohwinkel syndrome Disease MeSH Browser

Winkelman Bethge Pfeiffer syndrome Disease MeSH Browser

Wolfram Syndrome 2 Disease MeSH Browser

Wolfram Syndrome, Mitochondrial Form Disease MeSH Browser