Hirschsprung Disease [Hirschsprungova nemoc]

topical
102
Terms

aganglionosis coli
aganglionóza
Hirschprungova choroba
megacolon congenitum
rektosigmoidální aganglionóza
střevní aganglionóza
vrozená intestinální aganglionóza

 

Aganglionic Megacolon
Aganglionosis, Colonic
Aganglionosis, Rectosigmoid Colon
Aganglionosis, Total Colonic
Colonic Aganglionosis
Congenital Intestinal Aganglionosis
Congenital Megacolon
Hirschsprung's Disease
Megacolon, Aganglionic
Megacolon, Congenital
Rectosigmoid Aganglionosis
Total Colonic Aganglionosis

Persistent link   https://www.medvik.cz/link/D006627
Definition

Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.

Annotation
acquired megacolon = MEGACOLON
DUI
D006627 MeSH Browser
CUI
M0010379
Previous indexing
Megacolon (1966-1982)
History note
83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82
Online note
search MEGACOLON 1966-82
Public note
83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82