Myeloproliferative Disorders [myeloproliferativní poruchy]

topical
222
Terms

myeloproliferační poruchy
myeloproliferativní choroby
myeloproliferativní nemoci
myeloproliferativní onemocnění

Persistent link   https://www.medvik.cz/link/D009196
Definition

Conditions which cause proliferation of hemopoietically active tissue or of tissue which has embryonic hemopoietic potential. They all involve dysregulation of multipotent MYELOID PROGENITOR CELLS, most often caused by a mutation in the JAK2 PROTEIN TYROSINE KINASE.

Annotation
myelo- here = bone marrow, not spinal cord; general; prefer specifics
DUI
D009196 MeSH Browser
CUI
M0014332
History note
70(66)
Public note
70

C Diseases
C01 Infections 2 027
C04 Neoplasms 12 832
C11 Eye Diseases 1 495
C15.378.190 Bone Marrow Diseases 187
C15.378.190.250 Bone Marrow Neoplasms 50
C15.378.190.625 Myelodysplastic Syndromes 619
C15.378.190.636 Myeloproliferative Disorders 222
C15.378.190.636.085 Anemia, Myelophthisic
C15.378.190.636.276 Leukemia, Erythroblastic, Acute 57
C15.378.190.636.380 Leukemia, Neutrophilic, Chronic 7
C15.378.190.636.484 Leukemoid Reaction 8
C15.378.190.636.753 Polycythemia Vera 145
C15.378.190.636.765 Primary Myelofibrosis 132
C15.378.190.636.860 Thrombocytosis 61

Myeloproliferative Disease, Autosomal Recessive Disease MeSH Browser

Myeloproliferative Disorder, Chronic, with Eosinophilia Disease MeSH Browser

Transient Myeloproliferative Disorder of Down Syndrome Disease MeSH Browser