Polycythemia Vera [polycythaemia vera]

topical
145
Terms

Oslerova-Vaquezova nemoc
polycythaemia rubra vera
pravá polycytemie

 

Erythremia
Osler-Vaquez Disease
Polycythemia Ruba Vera
Polycythemia Rubra Vera
Primary Polycythemia

Persistent link   https://www.medvik.cz/link/D011087
Definition

A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs.

DUI
D011087 MeSH Browser
CUI
M0017168

C Diseases
C04 Neoplasms 12 832
C04.588.448 Hematologic Neoplasms 871
C04.588.448.200 Bone Marrow Neoplasms 50
C04.588.448.200.500 Polycythemia Vera 145
C15.378.190 Bone Marrow Diseases 187
C15.378.190.250 Bone Marrow Neoplasms 50
C15.378.190.250.500 Polycythemia Vera 145
C15.378.190.636 Myeloproliferative Disorders 222
C15.378.190.636.085 Anemia, Myelophthisic
C15.378.190.636.276 Leukemia, Erythroblastic, Acute 57
C15.378.190.636.380 Leukemia, Neutrophilic, Chronic 7
C15.378.190.636.484 Leukemoid Reaction 8
C15.378.190.636.753 Polycythemia Vera 145
C15.378.190.636.765 Primary Myelofibrosis 132
C15.378.190.636.860 Thrombocytosis 61
C15.378.400 Hematologic Neoplasms 871
C15.378.400.200 Bone Marrow Neoplasms 50
C15.378.400.200.500 Polycythemia Vera 145

Erythremia, Alpha-Globin Type Disease MeSH Browser

Erythremia, Beta-Globin Type Disease MeSH Browser