Osteopetrosis [Albers-Schönbergova nemoc]

topical
41
Terms

Albers-Schönbergova nemoc autosomálně dominantní
familiární osteopetróza
mramorová kostní choroba
mramorová kostní nemoc
nemoc mramorových kostí
osteopetróza kongenitální

 

Albers-Schoenberg Disease
Albers-Schonberg Disease
Albers-Schönberg Disease
Albers-Schonberg Disease, Autosomal Dominant
Autosomal Dominant Osteopetrosis Type 2
Congenital Osteopetrosis
Marble Bone Disease
Marble Bones, Autosomal Dominant
Osteopetrosis Autosomal Dominant Type 2
Osteopetrosis, Autosomal Dominant 2
Osteopetrosis, Autosomal Dominant, Type II
Osteosclerosis Fragilis
Osteosclerosis Fragilis Generalisata

Persistent link   https://www.medvik.cz/link/D010022
Definition

Excessive formation of dense trabecular bone leading to pathological fractures; OSTEITIS; SPLENOMEGALY with infarct; ANEMIA; and extramedullary hemopoiesis (HEMATOPOIESIS, EXTRAMEDULLARY).

Annotation
do not confuse with OSTEOPOROSIS
DUI
D010022 MeSH Browser
CUI
M0015549

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