osteopoikilóza [Osteopoikilosis]

tematický
6
Termíny

osteopathia condensans disseminata

Perzistentní odkaz   https://www.medvik.cz/link/D010023
Definice

Vzácné vrozené onemocnění charakterizované lokalizovaným ztluštěním spongiózy, zejm. v kostech končetin (karpus, tarsus). Syn. osteopathia condensans disseminata. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )

An asymptomatic, autosomal dominant trait in which pea-sized sclerotic spots, prominent in the metaphyseal area, are accompanied by unique cutaneous lesions. These are yellowish papules or plaques with increased elastin content. (From Cecil Textbook of Medicine, 19th ed, pp1434-35)

Anotace
a form of osteosclerosis
DUI
D010023 MeSH Prohlížeč
CUI
M0015550
Historická pozn.
91(64); was see under OSTEOSCLEROSIS 1970-90; was see under BONE DISEASES 1967-69
Veřejná pozn.
91; was see under OSTEOSCLEROSIS 1970-90; was see under BONE DISEASES 1967-69

C Nemoci
C05.116 nemoci kostí 796
C05.116.099.708 osteochondrodysplazie 125
C05.116.099.708.702 osteoskleróza 38
C05.116.099.708.702.593 meloreostóza 5
C05.116.099.708.702.678 Albers-Schönbergova nemoc 41
C05.116.099.708.702.685 osteopoikilóza 6
C17.300 nemoci pojiva 282
C17.300.116 anetodermie 5
C17.300.182 nemoci chrupavky 141
C17.300.185 celulitis 133
C17.300.200 kolagenózy 183
C17.300.230 cutis laxa 10
C17.300.250 dermatomyozitida 240
C17.300.428 homocystinurie 108
C17.300.451 lipedém 20
C17.300.500 Marfanův syndrom 105
C17.300.550 mucinózy 17
C17.300.690 Noonanové syndrom 52
C17.300.705 osteopoikilóza 6
C17.300.710 panniculitis 43
C17.300.715 indurace penisu 48
C17.300.775 revmatické nemoci 2 182

Buschke-Ollendorff syndrome Disease MeSH Prohlížeč

Melorheostosis with Osteopoikilosis Disease MeSH Prohlížeč

Osteopoikilosis and dacryocystitis Disease MeSH Prohlížeč

Osteopoikilosis, Isolated Disease MeSH Prohlížeč