Osteopoikilosis [osteopoikilóza]

topical
6
Terms

osteopathia condensans disseminata

Persistent link   https://www.medvik.cz/link/D010023
Definition

An asymptomatic, autosomal dominant trait in which pea-sized sclerotic spots, prominent in the metaphyseal area, are accompanied by unique cutaneous lesions. These are yellowish papules or plaques with increased elastin content. (From Cecil Textbook of Medicine, 19th ed, pp1434-35)

Annotation
a form of osteosclerosis
DUI
D010023 MeSH Browser
CUI
M0015550
History note
91(64); was see under OSTEOSCLEROSIS 1970-90; was see under BONE DISEASES 1967-69
Public note
91; was see under OSTEOSCLEROSIS 1970-90; was see under BONE DISEASES 1967-69

C Diseases
C05.116 Bone Diseases 796
C05.116.099.708 Osteochondrodysplasias 125
C05.116.099.708.702 Osteosclerosis 38
C05.116.099.708.702.593 Melorheostosis 5
C05.116.099.708.702.678 Osteopetrosis 41
C05.116.099.708.702.685 Osteopoikilosis 6
C17.300.116 Anetoderma 5
C17.300.182 Cartilage Diseases 141
C17.300.185 Cellulitis 134
C17.300.200 Collagen Diseases 183
C17.300.230 Cutis Laxa 10
C17.300.250 Dermatomyositis 240
C17.300.428 Homocystinuria 108
C17.300.451 Lipedema 20
C17.300.500 Marfan Syndrome 105
C17.300.550 Mucinoses 17
C17.300.690 Noonan Syndrome 52
C17.300.705 Osteopoikilosis 6
C17.300.710 Panniculitis 43
C17.300.715 Penile Induration 48
C17.300.775 Rheumatic Diseases 2 184
C17.300.799 Scleroderma, Systemic 487

Buschke-Ollendorff syndrome Disease MeSH Browser

Melorheostosis with Osteopoikilosis Disease MeSH Browser

Osteopoikilosis and dacryocystitis Disease MeSH Browser

Osteopoikilosis, Isolated Disease MeSH Browser