sfingomyelinfosfodiesterasa [Sphingomyelin Phosphodiesterase]

tematický
21
Termíny

sfingomyelinasa
sfingomyelinasa C
sfingomyelináza
sfingomyelináza C
sfingomyelinfosfodiesteráza

 

Sphingomyelin Cholinephosphohydrolase
Sphingomyelin Cleaving Enzyme
Sphingomyelinase
Sphingomyelinase C

Perzistentní odkaz   https://www.medvik.cz/link/D013108
Definice

Enzym, který katalyzuje hydrolýzu sfingomyelinu na ceramid (N-acylsfingosin) a cholinfosfát. Defekt tohoto enzymu vede k Niemannově-Pickově nemoci. EC 3.1.4.12.

An enzyme that catalyzes the hydrolysis of sphingomyelin to ceramide (N-acylsphingosine) plus choline phosphate. A defect in this enzyme leads to NIEMANN-PICK DISEASE. EC 3.1.4.12.

Anotace
/defic: consider also NIEMANN-PICK DISEASE
DUI
D013108 MeSH Prohlížeč
CUI
M0020300
CAS
Sphingomyelin cholinephosphohydrolase
Předchozí užití
Phosphodiesterases (1973-1974); Sphingomyelins (1973-1974)
Historická pozn.
91(75); was see under PHOSPHODIESTERASES 1975-90
Veřejná pozn.
91; was see under PHOSPHODIESTERASES 1975-90

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