Polycystic Kidney, Autosomal Recessive [polycystické ledviny autozomálně recesivní]

topical
29
Terms

autozomálně recesivní polycystická choroba ledvin
autozomálně recesivní polycystické ledviny
infantilní polycystická choroba ledvin, typ 1
infantilní polycystické ledviny, typ 1

 

ARPKD
Autosomal Recessive Polycystic Kidney
Autosomal Recessive Polycystic Kidney Disease
Kidney, Polycystic, Autosomal Recessive
Polycystic Kidney and Hepatic Disease 1
Polycystic Kidney and Hepatic Disease 1 (Autosomal Recessive)
Polycystic Kidney Disease, Autosomal Recessive
Polycystic Kidney Disease, Infantile, Type 1
Polycystic Kidney Disease, Infantile, Type I

Persistent link   https://www.medvik.cz/link/D017044
Definition

A genetic disorder with autosomal recessive inheritance, characterized by multiple CYSTS in both KIDNEYS and associated LIVER lesions. Serious manifestations are usually present at BIRTH with high PERINATAL MORTALITY.

DUI
D017044 MeSH Browser
CUI
M0025899
Previous indexing
Kidney, Polycystic (1966-1991)
History note
1992
Public note
1992; see KIDNEY, POLYCYCSTIC, AUTOSOMAL RECESSIVE 1992-2000

C Diseases
C12.050.351.968 Urologic Diseases 836
C12.050.351.968.419 Kidney Diseases 3 067
C12.050.351.968.419.403 Kidney Diseases, Cystic 148
C12.050.351.968.419.403.875 Polycystic Kidney Diseases 83
C12.050.351.968.419.403.875.500 Polycystic Kidney, Autosomal Dominant 123
C12.050.351.968.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C12.200.777 Urologic Diseases 836
C12.200.777.419 Kidney Diseases 3 067
C12.200.777.419.403 Kidney Diseases, Cystic 148
C12.200.777.419.403.875 Polycystic Kidney Diseases 83
C12.200.777.419.403.875.500 Polycystic Kidney, Autosomal Dominant 123
C12.200.777.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C12.950.419 Kidney Diseases 3 067
C12.950.419.403 Kidney Diseases, Cystic 148
C12.950.419.403.875 Polycystic Kidney Diseases 83
C12.950.419.403.875.500 Polycystic Kidney, Autosomal Dominant 123
C12.950.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C16.131.077.717 Polycystic Kidney Diseases 83
C16.320.184 Ciliopathies 9
C16.320.184.625 Polycystic Kidney Diseases 83

Polycystic Kidney Disease, Potter Type I, with Microbrachycephaly, Hypertelorism, and Brachymelia Disease MeSH Browser

Polycystic kidneys, severe infantile with tuberous sclerosis Disease MeSH Browser

Renal dysplasia diffuse cystic Disease MeSH Browser