CREST Syndrome [CREST syndrom]

topical
6
Terms

kalcinóza, Raynaudův fenomén, ezofageální dysfunkce, sklerodaktylie a teleangiektázie
syndrom CREST
syndrom CRST

 

Calcinosis-Raynaud Phenomenon-Sclerodactyly-Telangiectasia
Calcinosis, Raynaud's phenomenon, Esophageal dismobility, Sclerodactyly, Telangiectasia Syndrome
CRST Syndrome

Persistent link   https://www.medvik.cz/link/D017675
Definition

A mild form of LIMITED SCLERODERMA, a multi-system disorder. Its features include symptoms of CALCINOSIS; RAYNAUD DISEASE; ESOPHAGEAL MOTILITY DISORDERS; sclerodactyly, and TELANGIECTASIS. When the defect in esophageal function is not prominent, it is known as CRST syndrome.

Annotation
CREST syndrome: an acronym for Calcinosis, Raynaud phenomenon, Esophageal dysfunction, Sclerodactyly, Telangiectasis
DUI
D017675 MeSH Browser
CUI
M0026732
Previous indexing
Calcinosis (1975-1993); Raynaud's Disease (1975-1993); Scleroderma, Systemic (1975-1993)
History note
1994
Public note
1994

C Diseases
C06.405.117 Esophageal Diseases 299
C06.405.117.119 Deglutition Disorders 550
C06.405.117.119.500 Esophageal Motility Disorders 92
C06.405.117.119.500.204 CREST Syndrome 6
C06.405.117.119.500.432 Esophageal Achalasia 200
C06.405.117.119.500.450 Esophageal Spasm, Diffuse 3
C06.405.117.119.500.484 Gastroesophageal Reflux 974
C06.405.117.119.500.742 Plummer-Vinson Syndrome 10
C14.907 Vascular Diseases 1 789
C14.907.355.830 Thrombosis 1 663
C14.907.355.830.573 Livedoid Vasculopathy
C14.907.355.830.573.750 Raynaud Disease 193
C14.907.355.830.573.750.500 CREST Syndrome 6
C14.907.617.812 Raynaud Disease 193
C14.907.617.812.500 CREST Syndrome 6
C14.907.823 Telangiectasis 57
C14.907.823.213 Ataxia Telangiectasia 47
C14.907.823.225 CREST Syndrome 6
C14.907.823.502 Retinal Telangiectasis 3
C17.300.799 Scleroderma, Systemic 482
C17.300.799.801 Scleroderma, Limited 2
C17.300.799.801.500 CREST Syndrome 6
C17.800 Skin Diseases 2 796
C17.800.784 Scleroderma, Systemic 482
C17.800.784.801 Scleroderma, Limited 2
C17.800.784.801.500 CREST Syndrome 6
C17.800.862.406 Livedoid Vasculopathy
C17.800.862.406.750 Raynaud Disease 193
C17.800.862.406.750.500 CREST Syndrome 6
C18.452 Metabolic Diseases 1 196
C18.452.174.130 Calcinosis 380
C18.452.174.130.093 Calcinosis Cutis
C18.452.174.130.186 Calciphylaxis 51
C18.452.174.130.204 CREST Syndrome 6
C18.452.174.130.560 Nephrocalcinosis 46
C18.452.174.130.780 Vascular Calcification 44