N-Acetylgalactosamine-4-Sulfatase [arylsulfatasa B]
- Terms
-
arylsulfatasa B1
arylsulfatasa B2
arylsulfatáza B
arylsulfatáza B1
arylsulfatáza B2
N-acetylgalaktosamin-4-sulfatasa
N-acetylgalaktosamin-4-sulfatáza
-
Arylsulfatase B
Arylsulfatase B1
Arylsulfatase B2
N-Acetylgalactosamine 4-Sulfatase
N-Acetylgalactosamine-4-sulfate Sulfatase
N-Acetylgalactosamine-4-sulphate Sulphatase
An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.
- DUI
- D020051 MeSH Browser
- CUI
- M0029765
- CAS
- N-Acetyl-D-Galactosamine-4-sulfate 4-sulfohydrolase
- Previous indexing
- Sulfatases (1988-1998)
- History note
- 1999; for ARYLSULFATASE B use CHONDRO-4-SULFATASE 1975-1998; use N-ACETYLGALACTOSAMINE-4-SULFATASE (NM) 1988-1998
- Public note
- 1999; for ARYLSULFATASE B see CHONDRO-4-SULFATASE 1975-1998; N-ACETYLGALACTOSAMINE-4-SULFATE SULFATASE (now N-ACETYLGALACTOSAMINE-4-SULFATASE) was indexed under SULFATASES 1988-1998
Combination
- deficiency
- Mucopolysaccharidosis VI
Allowable subheadings
- AD
- administration & dosage
- AE
- adverse effects
- AN
- analysis
- AI
- antagonists & inhibitors
- BI
- biosynthesis
- BL
- blood
- CF
- cerebrospinal fluid
- CS
- chemical synthesis
- CH
- chemistry
- CL
- classification
- DE
- drug effects
- EC
- economics
- GE
- genetics
- HI
- history
- IM
- immunology
- IP
- isolation & purification
- ME
- metabolism
- PK
- pharmacokinetics
- PD
- pharmacology
- PH
- physiology
- PO
- poisoning
- RE
- radiation effects
- ST
- standards
- SD
- supply & distribution
- TU
- therapeutic use 2
- TO
- toxicity
- UL
- ultrastructure
- UR
- urine
ARSB protein, human Chemical MeSH Browser
galsulfase Chemical MeSH Browser