Succinate-Semialdehyde Dehydrogenase [sukcinátsemialdehyddehydrogenasa]

topical
1
Terms

sukcinátsemialdehyddehydrogenáza

 

NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase

Persistent link   https://www.medvik.cz/link/D050644
Definition

An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).

DUI
D050644 MeSH Browser
CUI
M0079133
History note
2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979
Public note
2006; SUCCINATE-SEMIALDEHYDE DEHYDROGENASE was indexed under ALDEHYDE OXIDOREDUCTASES 1977-2005

D Chemicals and Drugs
D08.811 Enzymes 1 547
D08.811.682 Oxidoreductases 446
D08.811.682.657.163 Aldehyde Oxidoreductases 25
D08.811.682.657.163.249 Aldehyde Dehydrogenase 38
D08.811.682.657.163.311 Aldehyde Oxidase 4
D08.811.682.657.163.374 Aspartate-Semialdehyde Dehydrogenase 1
D08.811.682.657.163.468 Benzaldehyde Dehydrogenase (NADP+)
D08.811.682.657.163.515 Betaine-Aldehyde Dehydrogenase
D08.811.682.657.163.781 Glycolaldehyde Dehydrogenase 1
D08.811.682.657.163.843 Succinate-Semialdehyde Dehydrogenase 1
D10 Lipids 2 524

ALDH5A1 protein, human Chemical MeSH Browser

Aldh5a1 protein, mouse Chemical MeSH Browser

Aldh5a1 protein, rat Chemical MeSH Browser

gabD protein, E coli Chemical MeSH Browser