1-pyrrolin-5-karboxylátdehydrogenasa [1-Pyrroline-5-Carboxylate Dehydrogenase]

tematický
1
Termíny

Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
GGS Dehydrogenase
Glutamic-Gamma-Semialdehyde Dehydrogenase
Glutamyl-Gamma-Semialdehyde Dehydrogenase
NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase

Perzistentní odkaz   https://www.medvik.cz/link/D050842
Definice

Enzym, který katalyzuje oxidaci 1-pyrrolin-5-karboxylátu na L-glutamát v přítomnosti (koenzymu) NAD. Poruchy enzymu jsou příčinou hyperprolinémie II.

An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.

DUI
D050842 MeSH Prohlížeč
CUI
M0092808
Historická pozn.
2006(1981)
Veřejná pozn.
2006; 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE was indexed under AMINE OXIDOREDUCTASES 1981-2004