1-Pyrroline-5-Carboxylate Dehydrogenase [1-pyrrolin-5-karboxylátdehydrogenasa]

topical
1
Terms

Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
GGS Dehydrogenase
Glutamic-Gamma-Semialdehyde Dehydrogenase
Glutamyl-Gamma-Semialdehyde Dehydrogenase
NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase

Persistent link   https://www.medvik.cz/link/D050842
Definition

An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.

DUI
D050842 MeSH Browser
CUI
M0092808
History note
2006(1981)
Public note
2006; 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE was indexed under AMINE OXIDOREDUCTASES 1981-2004

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