Malignant Atrophic Papulosis [maligní atrofická papulóza]

topical
3
Terms

Degosova nemoc
Degosův syndrom
erythrokeratoderma en cocardes
maligní atrofická papulóza Degos

 

Degos Disease
Degos Syndrome
Degos's Malignant Atrophic Papulosis
Erythrokeratoderma en cocardes
Kohlmeier-Degos Disease
Papulosis, Malignant Atrophic

Persistent link   https://www.medvik.cz/link/D054853
Definition

Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.

Annotation
malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA
DUI
D054853 MeSH Browser
CUI
M0508347
History note
2008
Public note
2008

C Diseases
C14.907 Vascular Diseases 1 793
C14.907.137.126 Arteriosclerosis 2 351
C14.907.137.230 Carotid Stenosis 417
C14.907.137.372 Fibromuscular Dysplasia 25
C14.907.137.427 Leriche Syndrome 9
C14.907.137.615 Moyamoya Disease 26
C14.907.137.727 Renal Artery Obstruction 184
C14.907.137.780 Retinal Artery Occlusion 53
C14.907.137.870 Thromboangiitis Obliterans 66
C14.907.940 Vasculitis 480
C14.907.940.080 Aortitis 36
C14.907.940.090 Arteritis 88
C14.907.940.100 Behcet Syndrome 56
C14.907.940.320 Cogan Syndrome 6
C14.907.940.740 Phlebitis 113
C14.907.940.777 IgA Vasculitis 76
C14.907.940.815 Retinal Vasculitis 19
C14.907.940.890 Shwartzman Phenomenon 10
C14.907.940.897 Systemic Vasculitis 18
C14.907.940.905 Thromboangiitis Obliterans 66
C17.800 Skin Diseases 2 801
C17.800.862.060 Angiomatosis, Bacillary 5
C17.800.862.150 Behcet Syndrome 56
C17.800.862.201 Cryoglobulinemia 72
C17.800.862.252 Giant Cell Arteritis 139
C17.800.862.329 IgA Vasculitis 76
C17.800.862.406 Livedoid Vasculopathy
C17.800.862.625 Polyarteritis Nodosa 92
C17.800.862.675 Pyoderma Gangrenosum 78
C17.800.862.775 Sneddon Syndrome 2
C17.800.862.875 Takayasu Arteritis 94
C17.800.862.945 Urticaria 301