Kasabach-Merritt Syndrome [syndrom Kasabachův-Merrittové]

topical
3
Terms

Kasabach-Merittové syndrom
syndrom Kasabach-Merittové

 

Hemangioma Thrombocytopenia Syndrome
Hemangioma-Thrombocytopenia Syndrome
Kasabach-Merritt Phenomenon
Thrombocytopenia-Hemangioma Syndrome

Persistent link   https://www.medvik.cz/link/D059885
Definition

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

DUI
D059885 MeSH Browser
CUI
M0551903
Previous indexing
Hemangioendothelioma (1979-2011); Hemangioma (1964-2011)
History note
2012
Public note
2012

C Diseases
C04 Neoplasms 12 832
C04.557.645.375 Hemangioma 446
C04.557.645.375.370 Hemangioendothelioma 26
C04.557.645.375.380 Hemangioma, Capillary 29
C04.557.645.375.385 Hemangioma, Cavernous 53
C04.557.645.375.617 Kasabach-Merritt Syndrome 3
C04.557.645.375.850 Sturge-Weber Syndrome 26
C15.378.140.855 Thrombocytopenia 603
C15.378.140.855.645 Kasabach-Merritt Syndrome 3
C15.378.140.855.925 Thrombotic Microangiopathies 62
C15.378.243 Cytopenia 3
C15.378.243.937 Thrombocytopenia 603
C15.378.243.937.645 Kasabach-Merritt Syndrome 3
C15.378.243.937.925 Thrombotic Microangiopathies 62

Kaposiform Hemangioendothelioma Disease MeSH Browser