filaminy [Filamins]

tematický
4
Termíny

filamin
filamin 1
filamin A
filamin B
filamin C
merofilaminy

 

280 kDa Actin-Binding Protein
alpha-Filamin
beta-Filamin
Filamin
Filamin 1
Filamin 1-Like Protein
Filamin A
Filamin B
Filamin C
Merofilamins

Perzistentní odkaz   https://www.medvik.cz/link/D064448
Definice

Rodina proteinů, které stabilizují aktinový cytoskelet. Jsou kódované různými geny FLN. Filaminy se účastní buněčné adheze a pohybu, vážou více než 90 vazebných partnerů (iontových kanálů, receptorů, intracelulárních signálních molekul a transkripčních faktorů). Mutace genů FLN vedou k anomáliím různé závažnosti.

A family of crosslinking filament proteins encoded by distinct FLN genes. Filamins are involved in cell adhesion, spreading, and migration, acting as scaffolds for over 90 binding partners including channels, receptors, intracellular signaling molecules and transcription factors. Due to the range of molecular interactions, mutations in FLN genes result in anomalies with moderate to lethal consequences.

DUI
D064448 MeSH Prohlížeč
CUI
M0061356
Historická pozn.
2014
Veřejná pozn.
2014; was indexed under CONTRACTILE PROTEINS and MICROFILAMENT PROTEINS 1977-2013.

A Anatomie
A11 buňky 976
A11.284.430.214 cytoplazma 364
A11.284.430.214.190 cytoplazmatické struktury 21
A11.284.430.214.190.750 cytoskelet 232
A11.284.430.214.190.750.050 mikrofilamenta 63
A11.284.430.214.190.750.050.414 filaminy 4
A11.284.430.214.190.750.050.830 kontraktilní svazky 3

D Chemikálie a léčiva
D05.750 polymery 1 053
D05.750.078 biopolymery 96
D05.750.078.730 mikrofilamentové proteiny 52
D05.750.078.730.032 aktin zastřešující proteiny 1
D05.750.078.730.248 aktinin 11
D05.750.078.730.250 aktiny 292
D05.750.078.730.266 calponiny 1
D05.750.078.730.281 kortaktin 1
D05.750.078.730.315 filaminy 4
D05.750.078.730.333 forminy 2
D05.750.078.730.350 gelsolin 5
D05.750.078.730.475 myosiny 132
D05.750.078.730.556 protein MARCKS
D05.750.078.730.637 profiliny 10
D05.750.078.730.719 tensiny 1
D05.750.078.730.800 tropomyosin 23
D05.750.078.730.825 troponin 263
D12.776 proteiny 2 575
D12.776.210.249 filaminy 4
D12.776.210.500 svalové proteiny 133
D12.776.220.525 mikrofilamentové proteiny 52
D12.776.220.525.032 aktin zastřešující proteiny 1
D12.776.220.525.250 aktinin 11
D12.776.220.525.255 aktiny 292
D12.776.220.525.268 calponiny 1
D12.776.220.525.281 kortaktin 1
D12.776.220.525.315 filaminy 4
D12.776.220.525.333 forminy 2
D12.776.220.525.350 gelsolin 5
D12.776.220.525.475 myosiny 132
D12.776.220.525.556 protein MARCKS
D12.776.220.525.637 profiliny 10
D12.776.220.525.719 tensiny 1
D12.776.220.525.800 tropomyosin 23
D12.776.220.525.825 troponin 263