- MeSH
- artritida diagnóza etiologie imunologie klasifikace mikrobiologie MeSH
- myozitida diagnóza etiologie klasifikace MeSH
- osteoartróza diagnóza farmakoterapie klasifikace MeSH
- revmatoidní artritida diagnostické zobrazování diagnóza farmakoterapie MeSH
- revmatologie * klasifikace MeSH
- spondylartritida diagnóza etiologie klasifikace MeSH
- systémový lupus erythematodes diagnóza klasifikace komplikace MeSH
- vaskulitida diagnóza etiologie klasifikace MeSH
- Publikační typ
- přehledy MeSH
OBJECTIVE: Granulomatosis with polyangiitis (GPA) is an ANCA-associated vasculitis. The 2022 ACR/EULAR-endorsed classification criteria for GPA was derived using data only from adult patients. We aimed to assess the performance of the ACR/EULAR classification criteria for GPA in paediatric patients and compare it with the EULAR/Pediatric Rheumatology International Trials Organization (PRINTO)/Pediatric Rheumatology European Society (PReS)-endorsed Ankara 2008 criteria for GPA. METHODS: Retrospective data of paediatric patients with GPA in 20 centres from 9 countries were evaluated. The diagnosis of GPA was made according to the expert opinion. The sensitivity, specificity, positive predictive value, and negative predictive value of the criteria sets were evaluated. RESULTS: The study included 77 patients with GPA and 108 controls [IgA vasculitis (n = 44), Takayasu's arteritis (n = 20), microscopic polyangiitis (n = 16), polyarteritis nodosa (n = 14), Behçet's disease (n = 12), eosinophilic granulomatosis with polyangiitis (n = 1) and Cogan's syndrome (n = 1)] with a median age of 17.8 and 15.2 years, respectively. Among patients with GPA, constitutional symptoms (85.7%) and ENT involvement (79.2%) were the most common presentations. In the GPA group, 73 patients fulfilled the Ankara 2008 criteria and 69 the ACR/EULAR classification criteria. Sensitivities of the Ankara 2008 criteria and the ACR/EULAR classification criteria were 94.8% and 89.6%, while specificities were 95.3% and 96.3%, respectively. No significant difference was found between sensitivities and specificities of both classification criteria (P = 0.229 and P = 0.733, respectively). CONCLUSION: In children, both the ACR/EULAR and EULAR/PRINTO/PReS Ankara 2008 classification criteria for GPA perform well and similarly.
- MeSH
- Behcetův syndrom klasifikace diagnóza MeSH
- Churgův-Straussové syndrom diagnóza klasifikace MeSH
- dítě MeSH
- granulomatóza s polyangiitidou * klasifikace diagnóza MeSH
- IgA vaskulitida diagnóza klasifikace MeSH
- lidé MeSH
- mikroskopická polyangiitida klasifikace diagnóza MeSH
- mladiství MeSH
- polyarteritis nodosa klasifikace diagnóza MeSH
- prediktivní hodnota testů MeSH
- předškolní dítě MeSH
- retrospektivní studie MeSH
- revmatologie normy MeSH
- senzitivita a specificita * MeSH
- Takayasuova arteriitida * klasifikace diagnóza MeSH
- Check Tag
- dítě MeSH
- lidé MeSH
- mladiství MeSH
- mužské pohlaví MeSH
- předškolní dítě MeSH
- ženské pohlaví MeSH
- Publikační typ
- časopisecké články MeSH
- multicentrická studie MeSH
- srovnávací studie MeSH
- Geografické názvy
- Evropa MeSH
- MeSH
- antifosfolipidový syndrom diagnóza MeSH
- diseminovaná intravaskulární koagulace diagnóza komplikace MeSH
- HELLP syndrom diagnóza MeSH
- hematologie * metody MeSH
- infarkt myokardu bez ST elevací diagnóza MeSH
- kongresy jako téma MeSH
- krevní obraz metody MeSH
- lidé MeSH
- spinální epidurální hematom diagnóza komplikace terapie MeSH
- trombocytopenie * diagnóza etiologie terapie MeSH
- Check Tag
- lidé MeSH
- MeSH
- hematologie MeSH
- mnohočetný myelom MeSH
- vnitřní lékařství * MeSH
- Publikační typ
- biografie MeSH
- oslavné články MeSH
In 2021, the Kidney Disease: Improving Global Outcomes (KDIGO) Guideline for the Management of Glomerular Diseases was published. KDIGO is committed to providing the nephrology community with periodic updates, based on new developments for each disease. For patients with anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV), avacopan received regulatory approval in late 2021, leading to this KDIGO guideline update. In addition, the evidence supporting a lower-dose glucocorticoid induction regimen or even complete replacement of glucocorticoids has become stronger. Herein, an executive summary of the most important guideline changes from the AAV chapter is provided as a quick reference.
- MeSH
- ANCA-asociované vaskulitidy * diagnóza farmakoterapie MeSH
- glomerulonefritida * diagnóza farmakoterapie MeSH
- glukokortikoidy terapeutické užití MeSH
- ledviny MeSH
- lidé MeSH
- nefrologie * MeSH
- protilátky proti cytoplazmě neutrofilů MeSH
- Check Tag
- lidé MeSH
- Publikační typ
- směrnice pro lékařskou praxi MeSH
- MeSH
- biomedicínské technologie organizace a řízení trendy MeSH
- cévní mozková příhoda terapie MeSH
- dostupnost zdravotnických služeb trendy MeSH
- kardiologie organizace a řízení trendy výchova MeSH
- lidé MeSH
- nádory prostaty prevence a kontrola MeSH
- osteoporóza prevence a kontrola MeSH
- paliativní péče organizace a řízení trendy MeSH
- praktické lékařství organizace a řízení trendy MeSH
- řízení zdravotnických informací organizace a řízení MeSH
- screeningové diagnostické programy organizace a řízení MeSH
- urgentní zdravotnické služby metody trendy MeSH
- zdravotnické služby * trendy MeSH
- Check Tag
- lidé MeSH
- Publikační typ
- novinové články MeSH
The current treatment algorithm for chronic thromboembolic pulmonary hypertension (CTEPH) as depicted in the 2022 European Society of Cardiology (ESC)/European Respiratory Society (ERS) guidelines on the diagnosis and treatment of pulmonary hypertension (PH) includes a multimodal approach of combinations of pulmonary endarterectomy (PEA), balloon pulmonary angioplasty (BPA) and medical therapies to target major vessel pulmonary vascular lesions, and microvasculopathy. Today, BPA of >1700 patients has been reported in the literature from centers in Asia, the US, and also Europe; many more patients have been treated outside literature reports. As BPA becomes part of routine care of patients with CTEPH, benchmarks for safe and effective care delivery become increasingly important. In light of this development, the ESC Working Group on Pulmonary Circulation and Right Ventricular Function has decided to publish a document that helps standardize BPA to meet the need of uniformity in patient selection, procedural planning, technical approach, materials and devices, treatment goals, complications including their management, and patient follow-up, thus complementing the guidelines. Delphi methodology was utilized for statements that were not evidence based. First, an anatomical nomenclature and a description of vascular lesions are provided. Second, treatment goals and definitions of complete BPA are outlined. Third, definitions of complications are presented which may be the basis for a standardized reporting in studies involving BPA. The document is intended to serve as a companion to the official ESC/ERS guidelines.
- MeSH
- arteria pulmonalis chirurgie MeSH
- balónková angioplastika * metody MeSH
- chronická nemoc MeSH
- funkce pravé komory srdeční MeSH
- kardiologie * MeSH
- lidé MeSH
- plicní embolie * komplikace terapie diagnóza MeSH
- plicní hypertenze * etiologie terapie diagnóza MeSH
- plicní oběh MeSH
- Check Tag
- lidé MeSH
- Publikační typ
- časopisecké články MeSH
The use of mechanical circulatory support using percutaneous ventricular assist devices (pVAD) has increased rapidly during the last decade without substantial new evidence for their effect on outcome. In addition, many gaps in knowledge still exist such as timing and duration of support, haemodynamic monitoring, management of complications, concomitant medical therapy, and weaning protocols. This clinical consensus statement summarizes the consensus of an expert panel of the Association for Acute CardioVascular Care, European Society of Intensive Care Medicine, European Extracorporeal Life Support Organization, and European Association for Cardio-Thoracic Surgery. It provides practical advice regarding the management of patients managed with pVAD in the intensive care unit based on existing evidence and consensus on best current practice.
- MeSH
- dospělí MeSH
- hrudní chirurgie * MeSH
- jednotky intenzivní péče MeSH
- kardiogenní šok terapie MeSH
- kardiologie * MeSH
- lidé MeSH
- mimotělní membránová oxygenace * metody MeSH
- péče o pacienty v kritickém stavu MeSH
- podpůrné srdeční systémy * MeSH
- Check Tag
- dospělí MeSH
- lidé MeSH
- Publikační typ
- časopisecké články MeSH
