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ECFS best practice guidelines: the 2018 revision
C. Castellani, AJA. Duff, SC. Bell, HGM. Heijerman, A. Munck, F. Ratjen, I. Sermet-Gaudelus, KW. Southern, J. Barben, PA. Flume, P. Hodková, N. Kashirskaya, MN. Kirszenbaum, S. Madge, H. Oxley, B. Plant, SJ. Schwarzenberg, AR. Smyth, G. Taccetti,...
Jazyk angličtina Země Nizozemsko
Typ dokumentu časopisecké články, přehledy
- MeSH
- cystická fibróza komplikace diagnóza terapie MeSH
- dítě MeSH
- dospělí MeSH
- kojenec MeSH
- lidé MeSH
- mladiství MeSH
- mladý dospělý MeSH
- novorozenec MeSH
- novorozenecký screening MeSH
- péče o umírající MeSH
- předškolní dítě MeSH
- směrnice pro lékařskou praxi jako téma MeSH
- sociální opora MeSH
- Check Tag
- dítě MeSH
- dospělí MeSH
- kojenec MeSH
- lidé MeSH
- mladiství MeSH
- mladý dospělý MeSH
- novorozenec MeSH
- předškolní dítě MeSH
- Publikační typ
- časopisecké články MeSH
- přehledy MeSH
- Geografické názvy
- Evropa MeSH
Developments in managing CF continue to drive dramatic improvements in survival. As newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of patients who have minimal lung disease on diagnosis. With the introduction of mutation-specific therapies and the prospect of truly personalised medicine, patients have the potential to enjoy good quality of life in adulthood with ever-increasing life expectancy. The landmark Standards of Care published in 2005 set out what high quality CF care is and how it can be delivered throughout Europe. This underwent a fundamental re-write in 2014, resulting in three documents; center framework, quality management and best practice guidelines. This document is a revision of the latter, updating standards for best practice in key aspects of CF care, in the context of a fast-moving and dynamic field. In continuing to give a broad overview of the standards expected for newborn screening, diagnosis, preventative treatment of lung disease, nutrition, complications, transplant/end of life care and psychological support, this consensus on best practice is expected to prove useful to clinical teams both in countries where CF care is developing and those with established CF centres. The document is an ECFS product and endorsed by the CF Network in ERN LUNG and CF Europe.
Adult Cystic Fibrosis Centre The Prince Charles Hospital Brisbane Australia
Cork Adult CF Centre Cork University Hospital University College Cork Republic of Ireland
Cystic Fibrosis Centre Azienda Ospedaliera Universitaria Integrata Verona Italy
Cystic Fibrosis Centre Gaslini Institute Genoa Italy
Cystic Fibrosis Centre Royal Brompton Hospital London UK
Department of Clinical and Health Psychology St James' University Hospital Leeds UK
Department of Clinical Psychology University Hospital Prague Czech Republic
Department of Pediatric Pulmunology CRCM Hôpital Necker Enfants Malades Paris France
Dept of Pulmonology University Medical Center Utrecht Utrecht The Netherlands
Division of Child Health Obstetrics and Gynaecology University of Nottingham Nottingham UK
Division of Pulmonary and Critical Care Medical University of South Carolina USA
Institute of Translational Medicine University of Liverpool Liverpool UK
Ostschweizer Kinderspital Sankt Gallen Claudiusstrasse 6 9006 St Gallen Switzerland
Regional Paediatric CF Unit Leeds General Infirmary Leeds UK
Citace poskytuje Crossref.org
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