Tripeptidyl-Peptidase 1 [tripeptidylpeptidasa 1]

topical
Terms

protein CLN2
protein TPP1
tripeptidylaminopeptidasa I
tripeptidylaminopeptidáza I
tripeptidylpeptidáza 1
tripeptidylpeptidáza I
tripeptidylproteasa 1
tripeptidylproteasa I
tripeptidylproteáza 1
tripeptidylproteáza I

 

CLN2 Protein
TPP1 Protein
Tripeptidyl Aminopeptidase I
Tripeptidyl Peptidase I
Tripeptidyl Protease I
Tripeptidyl-Peptidase I

Definition

Lysosomal Serine proteases that release N-terminal tripeptide from a polypeptide and cleave peptides between hydrophobic residues. An enzyme that in humans encoded by the TPP1 gene. It is involved in the degradation of bone collagen. Mutations in this gene are associated with the CEROID LIPOFUSCINOSIS, NEURONAL, 2; and SPINOCEREBELLAR ATAXIA, AUTOSOMAL RECESSIVE CEROID LIPOFUSCINOSIS, NEURONAL, 2; AND SPINOCEREBELLAR ATAXIA, AUTOSOMAL RECESSIVE 7.

DUI
D000091346 MeSH Browser
CUI
M000748625
History note
2022 (1993)
Public note
2022; TRIPEPTIDYL-PEPTIDASES 1 was indexed under AMINOPEPTIDASES, DIPEPTIDYL-PEPTIDYL-PEPTIDASES and under SERINE PROTEASES 1995-2021

D Chemicals and Drugs
D08.811 Enzymes 1 551
D08.811.277 Hydrolases 475
D08.811.277.656 Peptide Hydrolases 560
D08.811.277.656.350 Exopeptidases 4
D08.811.277.656.350.100 Aminopeptidases 112
D08.811.277.656.350.100.160 CD13 Antigens 6
D08.811.277.656.350.100.235 Cystinyl Aminopeptidase 13
D08.811.277.656.350.100.373 Glutamyl Aminopeptidase 1
D08.811.277.656.350.100.511 Leucyl Aminopeptidase 26
D08.811.277.656.350.100.633 Methionyl Aminopeptidases 1
D08.811.277.656.350.100.755 Pyroglutamyl-Peptidase I 1
D08.811.277.656.350.100.877 Tripeptidyl-Peptidase 1
D08.811.277.656.350.350.100 Cathepsin C 9
D08.811.277.656.350.350.126 Dipeptidyl Peptidase 4 85
D08.811.277.656.350.350.687 Peptidyl-Dipeptidase A 88
D08.811.277.656.350.350.843 Tripeptidyl-Peptidase 1
D08.811.277.656.959 Serine Proteases 21
D08.811.277.656.959.200 Cathepsin A 1
D08.811.277.656.959.250 Dipeptidyl Peptidase 4 85
D08.811.277.656.959.350 Serine Endopeptidases 138
D08.811.277.656.959.780 Tripeptidyl-Peptidase 1

TPP1 protein, human Chemical MeSH Browser

Tpp1 protein, mouse Chemical MeSH Browser

Tpp1 protein, rat Chemical MeSH Browser