Propionyl-Coenzyme A Carboxylase [propionyl-CoA-karboxylasa]
topical
- Terms
-
propionyl-CoA-karboxyláza
propionyl-koenzym A-karboxyláza
-
Propionyl-CoA Carboxylase
Persistent link
https://www.medvik.cz/link/D000095562
Definition
Mitochondrial carboxylase that is involved in the catabolism of odd chain fatty acids and branched amino acids. Dysfunction of propionyl-CoA carboxylase leads to the inherited metabolic disorder PROPIONIC ACIDEMIA. In bacteria it is an ATP-dependent carboxylase in CO2 fixation reactions where propionyl-CoA is converted to (S)-methylmalonyl-CoA.
- DUI
- D000095562 MeSH Browser
- CUI
- M000758637
- Previous indexing
- Methylmalonyl-CoA Decarboxylase (1979-2023)
- History note
- 2024; use Methylmalonyl-CoA Decarboxylase 2004-2023
- Public note
- 2024; see Methylmalonyl-CoA Decarboxylase 2004-2023
Combination
- deficiency
- Propionic Acidemia
Allowable subheadings
- AD
- administration & dosage
- AE
- adverse effects
- AN
- analysis
- AI
- antagonists & inhibitors
- BI
- biosynthesis
- BL
- blood
- CF
- cerebrospinal fluid
- CS
- chemical synthesis
- CH
- chemistry
- CL
- classification
- DE
- drug effects
- EC
- economics
- GE
- genetics
- HI
- history
- IM
- immunology
- IP
- isolation & purification
- ME
- metabolism
- PK
- pharmacokinetics
- PD
- pharmacology
- PH
- physiology
- PO
- poisoning
- RE
- radiation effects
- ST
- standards
- SD
- supply & distribution
- TU
- therapeutic use
- TO
- toxicity
- UL
- ultrastructure
- UR
- urine
...
Occurrences in Medvik records
D
Chemicals and Drugs
D08.811.464.257
Carbon-Carbon Ligases
D08.811.464.257.050.500
Propionyl-Coenzyme A Carboxylase