Carbamoyl-Phosphate Synthase (Ammonia) [karbamoylfosfátsynthasa (amoniak)]

topical
3
Terms

karbamoylfosfátsyntáza (amoniak)
karbamoylfosfátsyntetáza I
karbamoylfosfátsynthetasa I

 

Carbamoyl Phosphate Synthetase I
Carbamoyl-Phosphate Synthetase (Ammonia)
Carbamoyl-Phosphate Synthetase I
Carbamoylphosphate Synthetase I
Carbamyl Phosphate Synthase (Ammonia)
Carbamyl-Phosphate Synthase (Ammonia)
CP Synthase I

Persistent link   https://www.medvik.cz/link/D002222
Definition

An enzyme that catalyzes the formation of carbamoyl phosphate from ATP, carbon dioxide, and ammonia. This enzyme is specific for arginine biosynthesis or the urea cycle. Absence or lack of this enzyme may cause CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE. EC 6.3.4.16.

Annotation
/defic: consider CARBAMOYL-PHOSPHATE SYNTHETASE I DEFICIENCY DISEASE
DUI
D002222 MeSH Browser
CUI
M0003332
CAS
Carbon dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating)
Previous indexing
Phosphotransferases, ATP (1974); Ammonia (1974); Carbamates (1974)
History note
98(75)
Public note
98; see CARBAMYL PHOSPHATE SYNTHASE (AMMONIA) 1989-97; see LIGASES 1981-88; see PHOSPHOTRANSFERASES, ATP 1975-80

CPS1 protein, human Chemical MeSH Browser

Cps1 protein, mouse Chemical MeSH Browser

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