Cystathionine beta-Synthase [cystathionin-beta-synthasa]
topical
49
- Terms
-
cystathionin-beta-syntáza
cystationin-beta-syntáza
cystationinsyntetáza
-
beta-Thionase
Cystathionine Synthetase
Serine Sulfhydrase
Persistent link
https://www.medvik.cz/link/D003541
Definition
A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyzes the reaction of homocysteine with serine to form cystathionine with the elimination of water. Deficiency of this enzyme leads to HYPERHOMOCYSTEINEMIA and HOMOCYSTINURIA. EC 4.2.1.22.
- Annotation
- /defic: consider also HOMOCYSTINURIA or HYPERHOMOCYSTEINEMIA
- DUI
- D003541 MeSH Browser
- CUI
- M0005533
- CAS
- L-Serine hydro-lyase (adding homocysteine)
- Previous indexing
- Serine (1973-1974); Homocysteine (1973-1974); Hydro-Lyases (1973-1974)
- History note
- 1991(1975)
- Public note
- 1991; see HYDRO-LYASES 1975-1990
Allowable subheadings
- AD
- administration & dosage 1
- AE
- adverse effects
- AN
- analysis
- AI
- antagonists & inhibitors 1
- BI
- biosynthesis
- BL
- blood 2
- CF
- cerebrospinal fluid
- CS
- chemical synthesis
- CH
- chemistry 8
- CL
- classification
- DF
- deficiency 12
- DE
- drug effects 1
- EC
- economics
- GE
- genetics 29
- HI
- history
- IM
- immunology
- IP
- isolation & purification 2
- ME
- metabolism 21
- PK
- pharmacokinetics
- PD
- pharmacology
- PH
- physiology 1
- PO
- poisoning
- RE
- radiation effects
- ST
- standards
- SD
- supply & distribution
- TU
- therapeutic use 1
- TO
- toxicity
- UL
- ultrastructure
- UR
- urine 1
...
Occurrences in Medvik records
D
Chemicals and Drugs
D08.811.520.241.300.275
Enoyl-CoA Hydratase 2
D08.811.520.241.300.600
Prephenate Dehydratase
D08.811.520.241.300.650
Propanediol Dehydratase
D08.811.520.241.300.900
Urocanate Hydratase
CBSX2 protein, Arabidopsis Chemical MeSH Browser
CDCP2 protein, Arabidopsis Chemical MeSH Browser