uroporfyrinogen-III-synthetasa [Uroporphyrinogen III Synthetase]

tematický
1
Termíny

kosyntáza
kosynthasa
uroporfyrinogen-III-kosyntáza
uroporfyrinogen-III-kosyntetáza
uroporfyrinogen-III-kosynthetasa
uroporfyrinogen-III-syntáza
uroporfyrinogen-III-syntetáza
uroporfyrinogen-III-synthasa
uroporfyrinogenisomerasa

 

Cosynthase
Uroporphyrinogen III Cosynthetase
Uroporphyrinogen Isomerase
Uroporphyrinogen-III Synthase

Perzistentní odkaz   https://www.medvik.cz/link/D014576
Definice

Cytosolový enzym katalyzující vznik uroporfyrinogenu III z hydroxymethylbilanu. Gen je na 10. chromozomu. Mutace způsobuje kongenitální erytropoetickou porfyrii. (cit. Velký lékařský slovník online, 2017 http://lekarske.slovniky.cz)

An enzyme that catalyzes the cyclization of hydroxymethylbilane to yield UROPORPHYRINOGEN III and water. It is the fourth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by UROS gene. Mutations of UROS gene result in CONGENITAL ERYTHROPOIETIC PORPHYRIA.

DUI
D014576 MeSH Prohlížeč
CUI
M0022407
CAS
Hydroxymethylbilane hydro-lyase (cyclizing)
Předchozí užití
Porphobilinogen (1973-1974); Isomerases (1971-1974)
Historická pozn.
2005 (1975)
Veřejná pozn.
2005; see UROPORPHYRINOGEN-III SYNTHASE 1998-2004, see UROPORPHYRINOGEN III SYNTHASE 1991-1997, see HYDRO-LYASES 1985-1990, see ISOMERASES 1975-1984

D Chemikálie a léčiva
D08.811 enzymy 1 547
D08.811.520 lyasy 22
D08.811.520.241.300 dehydratasy 32
D08.811.520.241.300.050 akonitáthydratasa 8
D08.811.520.241.300.150 karboanhydrasy 52
D08.811.520.241.300.200 cystathionin-beta-synthasa 49
D08.811.520.241.300.250 enoyl-CoA-hydratasa 2
D08.811.520.241.300.275 enoyl-CoA-hydratáza 2
D08.811.520.241.300.287 syntázy mastných kyselin 13
D08.811.520.241.300.300 fumarasa 26
D08.811.520.241.300.500 fosfopyruváthydratasa 51
D08.811.520.241.300.550 porfobilinogensynthasa 10
D08.811.520.241.300.600 prefenátdehydratasa
D08.811.520.241.300.650 propandioldehydratasa
D08.811.520.241.300.850 tryptofansynthasa 2
D08.811.520.241.300.900 urokanasa
D08.811.520.241.300.950 uroporfyrinogen-III-synthetasa 1
D09 sacharidy 723
D10 lipidy 2 524