Glucosylceramidase [glukosylceramidasa]
- Terms
-
beta-glukocerebrosidasa
beta-glukocerebrosidáza
beta-glukocerebrozidáza
glukocerebrosidasa
glukocerebrosidáza
glukocerebrozidáza
glukosylceramidáza
glukozylceramidáza
kyselá beta-glukosidasa
kyselá beta-glukosidáza
kyselá beta-glukozidáza
-
Acid beta-Glucosidase
beta-Glucocerebrosidase
Glucocerebrosidase
Glucocerebroside beta-Glucosidase
Glucosyl Ceramidase
Glucosylceramide beta-Glucosidase
Glucosylsphingosine Glucosyl Hydrolase
A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in GAUCHER DISEASE. EC 3.2.1.45.
- Annotation
- /defic: consider also GAUCHER DISEASE
- DUI
- D005962 MeSH Browser
- CUI
- M0009360
- CAS
- D-Glucosyl-N-acylsphingosine glucosylhydrolase
- Previous indexing
- Glucose (1970-1974); Cerebrosides (1970-1974); Glycoside Hydrolases (1970-1974)
- History note
- 91(75); was see under GLUCOSIDASES 1975-90
- Public note
- 91; was see under GLUCOSIDASES 1975-90
Allowable subheadings
- AD
- administration & dosage 4
- AE
- adverse effects 1
- AN
- analysis 3
- AI
- antagonists & inhibitors
- BI
- biosynthesis 1
- BL
- blood
- CF
- cerebrospinal fluid 1
- CS
- chemical synthesis
- CH
- chemistry
- CL
- classification
- DF
- deficiency 7
- DE
- drug effects 1
- EC
- economics
- GE
- genetics 13
- HI
- history
- IM
- immunology
- IP
- isolation & purification 1
- ME
- metabolism 6
- PK
- pharmacokinetics
- PD
- pharmacology 1
- PH
- physiology
- PO
- poisoning
- RE
- radiation effects
- ST
- standards
- SD
- supply & distribution
- TU
- therapeutic use 8
- TO
- toxicity
- UL
- ultrastructure
- UR
- urine
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