Glycogen Debranching Enzyme System [enzymový systém rušící větvení glykogenu]

topical
3
Terms

enzym odbourávající větvení glykogenu
enzym rušící větvení glykogenu

 

Glycogen Debranching Enzyme
Transfer-Glucosidase

Persistent link   https://www.medvik.cz/link/D006004
Definition

1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.

Annotation
/defic: consider also GLYCOGEN STORAGE DISEASE TYPE III
DUI
D006004 MeSH Browser
CUI
M0009460
Previous indexing
Glucosidase (1973-1975); Glucosyltransferases (1973-1975); Glycogen (1973-1975)
History note
89(76); was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88
Online note
use GLYCOGEN DEBRANCHING ENZYME SYSTEM to search GLYCOGEN DEBRANCHING ENZYME 1976-88
Public note
89; was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88

D Chemicals and Drugs
D08.811 Enzymes 1 547
D08.811.277 Hydrolases 475
D08.811.277.450 Glycoside Hydrolases 88
D08.811.277.450.420 Glucosidases 46
D08.811.277.450.420.050 alpha-Glucosidases 81
D08.811.277.450.420.200 Cellulases 18
D08.811.277.450.420.375 Glucan 1,4-alpha-Glucosidase 7
D08.811.277.450.420.412 Glucosylceramidase 30
D08.811.277.450.420.450 Glycogen Debranching Enzyme System 3
D08.811.277.450.420.475 Lactase-Phlorizin Hydrolase 2
D08.811.913 Transferases 72
D08.811.913.400 Glycosyltransferases 48
D08.811.913.400.450 Hexosyltransferases 11
D08.811.913.400.450.460 Glucosyltransferases 58
D08.811.913.400.450.460.100 1,4-alpha-Glucan Branching Enzyme 2
D08.811.913.400.450.460.200 Chitin Synthase 5
D08.811.913.400.450.460.350 Glycogen Debranching Enzyme System 3
D08.811.913.400.450.460.375 Glycogen Synthase 8
D08.811.913.400.450.460.400 Phosphorylases 8
D08.811.913.400.450.460.750 Starch Synthase 3