Hemoglobinuria, Paroxysmal [paroxysmální hemoglobinurie]
- Terms
-
hemoglobinurie paroxysmální
paroxysmální chladová hemoglobinurie
paroxysmální noční hemoglobinurie
paroxyzmální chladová hemoglobinurie
paroxyzmální hemoglobinurie
paroxyzmální noční hemoglobinurie
syndrom Marchiafavův-Micheliho
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Marchiafava-Micheli Syndrome
Paroxysmal Cold Hemoglobinuria
Paroxysmal Hemoglobinuria
Paroxysmal Hemoglobinuria, Cold
Paroxysmal Hemoglobinuria, Nocturnal
Paroxysmal Nocturnal Hemoglobinuria
A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
- DUI
- D006457 MeSH Browser
- CUI
- M0010136
- History note
- 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
- Online note
- use HEMOGLOBINURIA, PAROXYSMAL to search MARCHIAFAVA-MICHELI SYNDROME 1966-77
- Public note
- 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
Allowable subheadings
- BL
- blood 6
- CF
- cerebrospinal fluid 0
- CI
- chemically induced 2
- CL
- classification 4
- CO
- complications 8
- CN
- congenital 0
- DI
- diagnosis 42
- DG
- diagnostic imaging 1
- DH
- diet therapy 0
- DT
- drug therapy 21
- EC
- economics 0
- EM
- embryology 0
- EN
- enzymology 1
- EP
- epidemiology 0
- EH
- ethnology 0
- ET
- etiology 15
- GE
- genetics 7
- HI
- history 1
- IM
- immunology 5
- ME
- metabolism 4
- MI
- microbiology 0
- MO
- mortality 0
- NU
- nursing 0
- PS
- parasitology 0
- PA
- pathology 8
- PP
- physiopathology 16
- PC
- prevention & control 0
- PX
- psychology 0
- RT
- radiotherapy 0
- RH
- rehabilitation 0
- SU
- surgery 0
- TH
- therapy 23
- UR
- urine 0
- VE
- veterinary 0
- VI
- virology 0