Iduronidase [iduronidasa]

topical
6
Terms

iduronidáza

 

alpha-L-Idosiduronase
alpha-L-Iduronidase

Persistent link   https://www.medvik.cz/link/D007068
Definition

An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.

Annotation
/defic: consider also MUCOPOLYSACCHARIDOSIS I
podheslo /nedostatek: zvaž také deskriptor MUKOPOLYSACHARIDÓZA I
DUI
D007068 MeSH Browser
CUI
M0010998
CAS
Glycosaminoglycan alpha-L-iduronohydrolase
Previous indexing
Glycoside Hydrolases (1972-1974); Hexoses (1972-1974); Uronic Acids (1972-1974)
History note
91(75); was see under GLYCOSIDE HYDROLASES 1975-90
Public note
91; was see under GLYCOSIDE HYDROLASES 1975-90

D Chemicals and Drugs
D08.811 Enzymes 1 549
D08.811.277 Hydrolases 475
D08.811.277.450 Glycoside Hydrolases 89
D08.811.277.450.050 alpha-L-Fucosidase 6
D08.811.277.450.066 Amylases 286
D08.811.277.450.114 beta-Fructofuranosidase 10
D08.811.277.450.207 Chitinases 54
D08.811.277.450.283 Dextranase
D08.811.277.450.329 Disaccharidases 27
D08.811.277.450.410 Galactosidases 45
D08.811.277.450.420 Glucosidases 46
D08.811.277.450.426 Glucuronidase 102
D08.811.277.450.430 N-Glycosyl Hydrolases 6
D08.811.277.450.483 Hexosaminidases 55
D08.811.277.450.529 Hyaluronoglucosaminidase 147
D08.811.277.450.560 Iduronidase 6
D08.811.277.450.585 Isoamylase 5
D08.811.277.450.625 Mannosidases 10
D08.811.277.450.642 Muramidase 219
D08.811.277.450.692 Neuraminidase 124
D08.811.277.450.770 Oligo-1,6-Glucosidase 1
D08.811.277.450.800 Polygalacturonase 20
D08.811.277.450.950 Xylosidases 11
D10 Lipids 2 526

D-idua protein, Drosophila Chemical MeSH Browser

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