Dermatofibrosarcoma [dermatofibrosarkom]

topical
30
Terms

Bednářův tumor
dermatofibrosarcoma protuberans
DFSP
juvenilní dermatofibrosarcoma protuberans
metastázující dermatofibrosarcoma protuberans
myxoidní dermatofibrosarcoma protuberans
obrovskobuněčný fibroblastom
pigmentovaný dermatofibrosarcoma protuberans

 

Bednar Tumor
Bednar's Tumor
Darier-Ferrand Tumor
Darier-Hoffmann Tumor
Dermatofibrosarcoma Protuberan
Dermatofibrosarcoma Protuberans, Familial
Dermatofibrosarcoma Protuberans, Fibrosarcomatous
Dermatofibrosarcoma Protuberans, Giant Cell
Dermatofibrosarcoma Protuberans, Myxoid
Dermatofibrosarcoma Protuberans, Pigmented
DFSP, Fibrosarcomatous
DFSP, Juvenile
DFSP, Myxoid
DFSP, Pigmented
Familial Dermatofibrosarcoma Protuberans
Fibrosarcomatous Dermatofibrosarcoma Protuberans
FS-DFSP
Giant Cell Fibroblastoma
Giant Dermatofibrosarcoma Protuberans
Metastatic Dermatofibrosarcoma Protuberans

Persistent link   https://www.medvik.cz/link/D018223
Definition

A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.

Annotation
coordinate with with SKIN NEOPLASMS
DUI
D018223 MeSH Browser
CUI
M0027452
Previous indexing
Fibrosarcoma (1966-1993); Skin Neoplasms (1966-1993)
History note
94
Public note
94

C Diseases
C04 Neoplasms 12 906
C04.557.450.565 Neoplasms, Connective Tissue 122
C04.557.450.565.590 Neoplasms, Fibrous Tissue 18
C04.557.450.565.590.350 Fibrosarcoma 151
C04.557.450.565.590.350.320 Dermatofibrosarcoma 30
C04.557.450.565.590.350.590 Neurofibrosarcoma 9
C04.557.450.795 Sarcoma 572
C04.557.450.795.350 Fibrosarcoma 151
C04.557.450.795.350.320 Dermatofibrosarcoma 30
C04.557.450.795.350.590 Neurofibrosarcoma 9