A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)

Annotation

"alveolar" has nothing to do with pulmonary alveoli: it refers to sac-like pathology of soft part; coordinate with precoordinated organ/neoplasm term

DUI

D018234 MeSH Browser

CUI

M0027463

Previous indexing

Sarcoma (1966-1993); Soft Tissue Neoplasms (1976-1993)

History note

1994

Public note

1994