Desmoplastic Small Round Cell Tumor [desmoplastický nádor z malých kulatých buněk]

topical
2
Terms

Desmoplastic Small Cell Tumor
Desmoplastic Small Round-Cell Tumor
Desmoplastic Small-Cell Tumor

Persistent link   https://www.medvik.cz/link/D058405
Definition

A rare, aggressive soft tissue sarcoma that primarily affects adolescents and young adults. It is most commonly found in the abdomen.

Annotation
coordinate IM with precoordinated organ/neoplasm term (IM)
DUI
D058405 MeSH Browser
CUI
M0542183
History note
2011
Public note
2011

C Diseases
C01 Infections 2 027
C04 Neoplasms 12 832
C04.557.450.795 Sarcoma 567
C04.557.450.795.135 Adenosarcoma 8
C04.557.450.795.290 Carcinosarcoma 26
C04.557.450.795.300 Chondrosarcoma 91
C04.557.450.795.332 Endometrial Stromal Tumors 11
C04.557.450.795.350 Fibrosarcoma 151
C04.557.450.795.390 Hemangiosarcoma 73
C04.557.450.795.400 Histiocytoma, Malignant Fibrous 17
C04.557.450.795.455 Leiomyosarcoma 123
C04.557.450.795.465 Liposarcoma 74
C04.557.450.795.480 Lymphangiosarcoma 8
C04.557.450.795.530 Mixed Tumor, Mesodermal 1
C04.557.450.795.550 Myosarcoma 4
C04.557.450.795.560 Myxosarcoma 7
C04.557.450.795.620 Osteosarcoma 203
C04.557.450.795.650 Phyllodes Tumor 34
C04.557.450.795.775 Sarcoma, Alveolar Soft Part 14
C04.557.450.795.800 Sarcoma, Clear Cell 9
C04.557.450.795.830 Sarcoma, Experimental 150
C04.557.450.795.850 Sarcoma, Kaposi 107
C04.557.450.795.853 Sarcoma, Myeloid 9
C04.557.450.795.870 Sarcoma, Small Cell 3
C04.557.450.795.875 Sarcoma, Synovial 37
C11 Eye Diseases 1 495