Erdheim-Chester Disease [Erdheimova-Chesterova nemoc]

topical
39
Terms

Erdheimova-Chesterova choroba

 

Granulomatosis, Lipid

Persistent link   https://www.medvik.cz/link/D031249
Definition

A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.

DUI
D031249 MeSH Browser
CUI
M0396932
Previous indexing
Histiocytosis (1989-2002); Histiocytosis, Langerhans-Cell (1988-2002); Histiocytosis, Non-Langerhans-Cell (1991-2002); Lipidosis (1979-2002); Xanthomatosis (1979-2002)
History note
2003
Public note
2003