gama-butyrobetaindioxygenasa [gamma-Butyrobetaine Dioxygenase]

tematický
Termíny

butyrobetainhydroxylasa
butyrobetainhydroxyláza
gama-butyrobetaindioxygenáza
gama-butyrobetainhydroxyláza
trimethylaminobutyráthydroxylasa

 

4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating)
Butyrobetaine Hydroxylase
gamma-Butyrobetaine Hydroxylase
gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase
gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase
Trimethylaminobutyrate Hydroxylase

Perzistentní odkaz   https://www.medvik.cz/link/D050563
Definice

Enzym, který katalyzuje hydroxylaci gama-butyrobetainu na L-karnitin. Je posledním enzymem v biosyntetické dráze L-karnitinu a je závislý na alfa-ketoglutarátu, železe, kyselině askorbové a kyslíku.

An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.

DUI
D050563 MeSH Prohlížeč
CUI
M0072677
Historická pozn.
2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974
Veřejná pozn.
2006; GAMMA-BUTYROBETAINE DIOXYGENASE was indexed under MIXED FUNCTION OXYGENASES 1980-2005, KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1980, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974

D Chemikálie a léčiva
D08.811 enzymy 1 547
D08.811.682 oxidoreduktasy 446
D08.811.682.690 oxygenasy 76
D08.811.682.690.708 oxygenasy se smíšenou funkcí 68
D08.811.682.690.708.062 benzoát-4-monooxygenasa
D08.811.682.690.708.125 katecholoxidasa 15
D08.811.682.690.708.170 systém (enzymů) cytochromů P-450 692
D08.811.682.690.708.292 dopamin-beta-hydroxylasa 52
D08.811.682.690.708.392 desaturasy mastných kyselin 44
D08.811.682.690.708.401 gama-butyrobetaindioxygenasa
D08.811.682.690.708.410 hemová oxygenasa (decyklizující) 24
D08.811.682.690.708.425 4-hydroxybenzoát-3-monooxygenasa
D08.811.682.690.708.557 kynurenin-3-monooxygenasa 1
D08.811.682.690.708.601 fenylalaninhydroxylasa 27
D08.811.682.690.708.660 lysinhydroxylasa 2
D08.811.682.690.708.694 prolyl-hydroxyláza 1
D08.811.682.690.708.715 cyklooxygenasy 40
D08.811.682.690.708.749 skvalenmonooxygenasa
D08.811.682.690.708.826 4-monooxygenasa kyseliny skořicové 1
D08.811.682.690.708.870 tryptofanhydroxylasa 3
D08.811.682.690.708.923 tyrosin-3-monooxygenasa 49
D08.811.682.690.708.961 epoxidreduktasy vitaminu K 7
D09 sacharidy 723
D10 lipidy 2 524