isovaleryl-CoA-dehydrogenasa [Isovaleryl-CoA Dehydrogenase]

tematický
2
Termíny

isovaleryl-CoA-dehydrogenáza
izovaleryl-CoA-dehydrogenáza

 

Isovaleryl CoA Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase

Perzistentní odkaz   https://www.medvik.cz/link/D050769
Definice

A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).

DUI
D050769 MeSH Prohlížeč
CUI
M0076387
RN
EC 1.3.8.4
Předchozí užití
Oxidoreductases Acting on CH-CH Group Donors (2004-2005); Oxidoreductases (1983-2003); Acyl Coenzyme A (1980-1982); Coenzyme A (1973-1980); Valerates (1973-1982)
Historická pozn.
2006(1973)
Veřejná pozn.
2006; ISOVALERYL-COA DEHYDROGENASE was indexed under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005, under OXIDOREDUCTASES 1983-2003, under ACYL COENZYME A 1980-1982, COENZYME A 1973-1980, and under VALERATES 1973-1982

D Chemikálie a léčiva
D08.811 enzymy 1 547
D08.811.682 oxidoreduktasy 446
D08.811.682.660.150 acyl-CoA-dehydrogenasy 6
D08.811.682.660.200 cholestenon-5-alfa-reduktasa 5
D08.811.682.660.250 koproporfyrinogenoxidasa 2
D08.811.682.660.275 dihydrodipikolinátreduktasa
D08.811.682.660.300 dihydroorotátoxidasa
D08.811.682.660.313 dihydroorotátdehydrogenasa 2
D08.811.682.660.385 respirační komplex II 20
D08.811.682.660.387 enoyl-ACP-reduktasa (NADH) 1
D08.811.682.660.425 glutaryl-CoA-dehydrogenasa 6
D08.811.682.660.462 isovaleryl-CoA-dehydrogenasa 2
D08.811.682.660.495 receptor laminu B
D08.811.682.660.500 prefenátdehydrogenasa
D08.811.682.660.600 protoporfyrinogenoxidasa 4
D09 sacharidy 723
D10 lipidy 2 523