Isovaleryl-CoA Dehydrogenase [isovaleryl-CoA-dehydrogenasa]

topical
2
Terms

isovaleryl-CoA-dehydrogenáza
izovaleryl-CoA-dehydrogenáza

 

Isovaleryl CoA Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase

Persistent link   https://www.medvik.cz/link/D050769
Definition

A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).

DUI
D050769 MeSH Browser
CUI
M0076387
Previous indexing
Oxidoreductases Acting on CH-CH Group Donors (2004-2005); Oxidoreductases (1983-2003); Acyl Coenzyme A (1980-1982); Coenzyme A (1973-1980); Valerates (1973-1982)
History note
2006(1973)
Public note
2006; ISOVALERYL-COA DEHYDROGENASE was indexed under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005, under OXIDOREDUCTASES 1983-2003, under ACYL COENZYME A 1980-1982, COENZYME A 1973-1980, and under VALERATES 1973-1982

D Chemicals and Drugs
D08.811 Enzymes 1 551
D08.811.682 Oxidoreductases 446
D08.811.682.660.150 Acyl-CoA Dehydrogenases 6
D08.811.682.660.200 Cholestenone 5 alpha-Reductase 5
D08.811.682.660.250 Coproporphyrinogen Oxidase 2
D08.811.682.660.300 Dihydroorotate Oxidase
D08.811.682.660.313 Dihydroorotate Dehydrogenase 2
D08.811.682.660.385 Electron Transport Complex II 20
D08.811.682.660.425 Glutaryl-CoA Dehydrogenase 6
D08.811.682.660.462 Isovaleryl-CoA Dehydrogenase 2
D08.811.682.660.495 Lamin B Receptor
D08.811.682.660.500 Prephenate Dehydrogenase
D08.811.682.660.600 Protoporphyrinogen Oxidase 5
D10 Lipids 2 528