Flavoproteinový enzym, který je zodpovědný za katabolismus lysinu, hydroxylysinu a tryptofanu. Katalyzuje oxidaci glutaryl-CoA na krotonoyl-CoA za použití FAD jako kofaktoru. Glutarová acidurie typu I je vrozená metabolická porucha způsobená nedostatkem glutaryl-CoA-dehydrogenázy.

A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.

DUI

D050770 MeSH Prohlížeč

CUI

M0074614

Předchozí užití

Oxidoreductases (1983-2003); Oxidoreductases Acting on CH-CH Group Donors (2004-2005); Acyl Coenzyme A (1973-1979); Coenzymes (1973-1979); Glutarates (1973-1980)

Historická pozn.

2006(1973)

Veřejná pozn.

2006; GLUTARYL-COA DEHYDROGENASE was indexed under ACYL COENZYME A 1973-1979; under GLUTARATES 1973-1982; and under COENZYME A 1973-1979; under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005