Glutaryl-CoA Dehydrogenase [glutaryl-CoA-dehydrogenasa]

topical
6
Terms

glutaryl-CoA-dehydrogenáza

 

Glutaryl CoA Dehydrogenase
Glutaryl-Coenzyme A Dehydrogenase

Persistent link   https://www.medvik.cz/link/D050770
Definition

A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.

DUI
D050770 MeSH Browser
CUI
M0074614
Previous indexing
Oxidoreductases Acting on CH-CH Group Donors (2004-2005); Oxidoreductases (1983-2003); Acyl Coenzyme A (1973-1979); Coenzymes (1973-1979); Glutarates (1973-1980)
History note
2006(1973)
Public note
2006; GLUTARYL-COA DEHYDROGENASE was indexed under ACYL COENZYME A 1973-1979; under GLUTARATES 1973-1982; and under COENZYME A 1973-1979; under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005

D Chemicals and Drugs
D08.811 Enzymes 1 547
D08.811.682 Oxidoreductases 446
D08.811.682.660.150 Acyl-CoA Dehydrogenases 6
D08.811.682.660.200 Cholestenone 5 alpha-Reductase 5
D08.811.682.660.250 Coproporphyrinogen Oxidase 2
D08.811.682.660.300 Dihydroorotate Oxidase
D08.811.682.660.313 Dihydroorotate Dehydrogenase 2
D08.811.682.660.385 Electron Transport Complex II 20
D08.811.682.660.425 Glutaryl-CoA Dehydrogenase 6
D08.811.682.660.462 Isovaleryl-CoA Dehydrogenase 2
D08.811.682.660.495 Lamin B Receptor
D08.811.682.660.500 Prephenate Dehydrogenase
D08.811.682.660.600 Protoporphyrinogen Oxidase 5
D10 Lipids 2 524