Idiopathic Pulmonary Fibrosis [idiopatická plicní fibróza]

topical
278
Terms

familiární idiopatická plicní fibróza
idiopatická plicní fibróza familiární
intersticiální plicní fibróza
IPF
kryptogenní fibrotizující alveolitida
kryptogenní fibrózující alveolitida
obvyklá intersticiální pneumonie

 

Cryptogenic Fibrosing Alveolitis
Familial Idiopathic Pulmonary Fibrosis
Fibrocystic Pulmonary Dysplasia
Fibrosing Alveolitis, Cryptogenic
Idiopathic Fibrosing Alveolitis, Chronic Form
Idiopathic Pulmonary Fibrosis, Familial
Interstitial Pneumonitis, Usual
Pulmonary Fibrosis, Idiopathic
Usual Interstitial Pneumonia

Persistent link   https://www.medvik.cz/link/D054990
Definition

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Annotation
PULMONARY FIBROSIS is also available
k dipozici je i deskriptor PLICNÍ FIBRÓZA
DUI
D054990 MeSH Browser
CUI
M0511887
Previous indexing
Pulmonary Fibrosis (1964-2008)
History note
2009
Public note
2009