Hereditary Angioedema Type III [hereditární angioedém typ III]

topical
5
Terms

dědičný angioedém typ III
dědičný angioedém typu III
estrogen-dependentní dědičný angioedém
hereditární angioedém typu III

 

Angioedema, Hereditary, Type III
Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function
Estrogen-Related HAE
Estrogen-Sensitive HAE
Estrogen-Sensitive Hereditary Angioedema
HAE with Normal C1 Inhibitor Concentration and Function
Hereditary Angioedema with Normal C1 Inhibitor Activity

Persistent link   https://www.medvik.cz/link/D056828
Definition

A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.

DUI
D056828 MeSH Browser
CUI
M0529317
Previous indexing
Angioedema (1964-2007); Angioedemas, Hereditary (2007-2009)
History note
2010
Public note
2010

C Diseases
C14.907 Vascular Diseases 1 793
C14.907.079 Angioedema 166
C14.907.079.500 Angioedemas, Hereditary 86
C14.907.079.500.500 Hereditary Angioedema Type III 5
C17.800 Skin Diseases 2 801
C17.800.862.945 Urticaria 301
C17.800.862.945.066 Angioedema 166
C17.800.862.945.066.500 Angioedemas, Hereditary 86
C17.800.862.945.066.500.500 Hereditary Angioedema Type III 5
C17.800.862.945.066.500.750 Hereditary Angioedema Types I and II 16
C20.543 Hypersensitivity 3 177
C20.543.480.904 Urticaria 301
C20.543.480.904.066 Angioedema 166
C20.543.480.904.066.500 Angioedemas, Hereditary 86
C20.543.480.904.066.500.500 Hereditary Angioedema Type III 5
C20.543.480.904.066.500.750 Hereditary Angioedema Types I and II 16